loading...| Preferred Name |
Subependymal giant cell astrocytoma |
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| Synonyms |
SEGA |
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| Definitions |
A rare low-grade astrocytoma characterized by a benign, slowly growing lesion typically arising in the wall of the lateral ventricles, composed of large ganglioid astrocytes. The tumor corresponds to WHO grade I and typically occurs during the first two decades of life in patients with tuberous sclerosis complex. Most patients present with worsening of epilepsy or symptoms of increased intracranial pressure. |
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| ID |
http://www.orpha.net/ORDO/Orphanet_251618 |
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| alternative_term |
SEGA |
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| definition |
A rare low-grade astrocytoma characterized by a benign, slowly growing lesion typically arising in the wall of the lateral ventricles, composed of large ganglioid astrocytes. The tumor corresponds to WHO grade I and typically occurs during the first two decades of life in patients with tuberous sclerosis complex. Most patients present with worsening of epilepsy or symptoms of increased intracranial pressure. |
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| definition_citation |
Orphanet |
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| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=251618 |
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| hasDbXref |
ICD-11:2A00.0Y UMLS:C0205768 ICD-10:D43.2 ICD-11:XH1L48 |
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| label |
Subependymal giant cell astrocytoma |
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| notation |
ORPHA:251618 |
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| part_of | ||
| prefixIRI |
ORDO:Orphanet_251618 |
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| prefLabel |
Subependymal giant cell astrocytoma |
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| treeView | ||
| subClassOf |