Preferred Name | Kawasaki disease | |
Synonyms |
Mucocutaneous lymph node syndrome |
|
Definitions |
A rare inflammatory disease characterized by an acute febrile, systemic, self-limiting, medium-vessel vasculitis primarily affecting children. It often causes acute coronary arteritis which is associated with coronary arterial aneurysms (CAA) that may be life threatening when untreated. |
|
ID |
http://www.orpha.net/ORDO/Orphanet_2331 |
|
alternative_term |
Mucocutaneous lymph node syndrome |
|
definition |
A rare inflammatory disease characterized by an acute febrile, systemic, self-limiting, medium-vessel vasculitis primarily affecting children. It often causes acute coronary arteritis which is associated with coronary arterial aneurysms (CAA) that may be life threatening when untreated. |
|
definition_citation |
Orphanet |
|
expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=2331 |
|
has_age_of_onset |
Adolescent Adult Childhood Infancy |
|
has_inheritance |
Multigenic/multifactorial |
|
hasDbXref |
ICD-11:4A44.5 MeSH:D009080 MedDRA:10023320 OMIM:611775 ICD-10:M30.3 UMLS:C0026691 |
|
label |
Kawasaki disease |
|
notation |
ORPHA:2331 |
|
part_of | ||
prefixIRI |
ORDO:Orphanet_2331 |
|
prefLabel |
Kawasaki disease |
|
present_in |
Worldwide AND has_point_prevalence_range : Unknown |
|
treeView | ||
subClassOf |