Preferred Name |
Limited systemic sclerosis |
|
Synonyms |
Systemic sclerosis sine scleroderma |
|
Definitions |
Limited systemic sclerosis (lSSc) (or SSc sine scleroderma) is a subset of systemic sclerosis (SSc; see this term) characterized by organ involvement in the absence of fibrosis of the skin. |
|
ID |
http://www.orpha.net/ORDO/Orphanet_220407 |
|
alternative_term |
Systemic sclerosis sine scleroderma |
|
definition |
Limited systemic sclerosis (lSSc) (or SSc sine scleroderma) is a subset of systemic sclerosis (SSc; see this term) characterized by organ involvement in the absence of fibrosis of the skin. |
|
definition_citation |
Orphanet |
|
expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=220407 |
|
has_age_of_onset |
Adult |
|
has_inheritance |
Not applicable |
|
hasDbXref |
ICD-11:4A42.2 ICD-10:M34.0 UMLS:C0748540 |
|
label |
Limited systemic sclerosis |
|
notation |
ORPHA:220407 Clinical subtype |
|
part_of | ||
prefixIRI |
ORDO:Orphanet_220407 |
|
prefLabel |
Limited systemic sclerosis |
|
present_in |
Worldwide AND has_cases/families_value : 200.0 (Case) Worldwide AND has_point_prevalence_range : Unknown |
|
treeView | ||
subClassOf |