loading...| Preferred Name | Idiopathic pulmonary fibrosis | |
| Synonyms |
IPF |
|
| Definitions |
An interstitial lung disease with a poor prognosis, that is characterized by the progressive formation of scar tissue within the lungs in the absence of any known cause. |
|
| ID |
http://www.orpha.net/ORDO/Orphanet_2032 |
|
| alternative_term |
IPF |
|
| definition |
An interstitial lung disease with a poor prognosis, that is characterized by the progressive formation of scar tissue within the lungs in the absence of any known cause. |
|
| definition_citation |
Orphanet |
|
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=2032 |
|
| has_age_of_onset |
Adult |
|
| has_inheritance |
Multigenic/multifactorial |
|
| hasDbXref |
OMIM:616373 OMIM:616371 OMIM:619611 ICD-10:J84.1 MedDRA:10021240 UMLS:C1800706 MeSH:D054990 ICD-11:CB03.4 OMIM:178500 |
|
| label |
Idiopathic pulmonary fibrosis |
|
| notation |
ORPHA:2032 |
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| part_of | ||
| prefixIRI |
ORDO:Orphanet_2032 |
|
| prefLabel |
Idiopathic pulmonary fibrosis |
|
| present_in |
Canada AND has_annual_incidence_average_value : 15.35 AND has_annual_incidence_range : 1-5 / 10 000 France AND has_annual_incidence_average_value : 2.8 AND has_annual_incidence_range : 1-9 / 100 000 United States AND has_point_prevalence_average_value : 6.7 AND has_point_prevalence_range : 1-9 / 100 000 Italy AND has_annual_incidence_average_value : 2.6 AND has_annual_incidence_range : 1-9 / 100 000 France AND has_point_prevalence_average_value : 8.2 AND has_point_prevalence_range : 1-9 / 100 000 Japan AND has_point_prevalence_average_value : 5.9 AND has_point_prevalence_range : 1-9 / 100 000 Worldwide AND has_point_prevalence_average_value : 16.125 AND has_point_prevalence_range : 1-5 / 10 000 United Kingdom AND has_annual_incidence_average_value : 1.2 AND has_annual_incidence_range : 1-9 / 100 000 Canada AND has_point_prevalence_average_value : 29.8 AND has_point_prevalence_range : 1-5 / 10 000 Finland AND has_annual_incidence_average_value : 1.3 AND has_annual_incidence_range : 1-9 / 100 000 Finland AND has_point_prevalence_average_value : 8.6 AND has_point_prevalence_range : 1-9 / 100 000 United States AND has_annual_incidence_average_value : 2.6 AND has_annual_incidence_range : 1-9 / 100 000 Worldwide AND has_annual_incidence_average_value : 5.55 AND has_annual_incidence_range : 1-9 / 100 000 Italy AND has_point_prevalence_average_value : 21.2 AND has_point_prevalence_range : 1-5 / 10 000 United Kingdom AND has_point_prevalence_average_value : 11.6 AND has_point_prevalence_range : 1-5 / 10 000 Korea, Republic of AND has_point_prevalence_average_value : 37.0 AND has_point_prevalence_range : 1-5 / 10 000 Korea, Republic of AND has_annual_incidence_average_value : 13.0 AND has_annual_incidence_range : 1-5 / 10 000 |
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| treeView | ||
| subClassOf |