loading...| Preferred Name | Dermatitis herpetiformis | |
| Synonyms |
Duhring-Brocq disease |
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| Definitions |
A chronic autoimmune subepidermal bullous disease characterized by grouped pruritic lesions such as papules, urticarial plaques, erythema, and herpetiform vesiculae, with a predominantly symmetrical distribution on extensor surfaces of the elbows (90%), knees (30%), shoulders, buttocks, sacral region, and face of children and adults. Erosions, excoriations and hyperpigmentation usually follow. It may also appear as a consequence of gluten intolerance. |
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| ID |
http://www.orpha.net/ORDO/Orphanet_1656 |
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| alternative_term |
Duhring-Brocq disease |
|
| definition |
A chronic autoimmune subepidermal bullous disease characterized by grouped pruritic lesions such as papules, urticarial plaques, erythema, and herpetiform vesiculae, with a predominantly symmetrical distribution on extensor surfaces of the elbows (90%), knees (30%), shoulders, buttocks, sacral region, and face of children and adults. Erosions, excoriations and hyperpigmentation usually follow. It may also appear as a consequence of gluten intolerance. |
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| definition_citation |
Orphanet |
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| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=1656 |
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| has_age_of_onset |
All ages |
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| has_inheritance |
Not applicable |
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| hasDbXref |
ICD-11:EB44 MeSH:D003874 ICD-10:L13.0 UMLS:C0011608 OMIM:601230 MedDRA:10012468 |
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| label |
Dermatitis herpetiformis |
|
| notation |
ORPHA:1656 |
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| part_of | ||
| prefixIRI |
ORDO:Orphanet_1656 |
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| prefLabel |
Dermatitis herpetiformis |
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| present_in |
Ireland AND has_annual_incidence_average_value : 1.5 AND has_annual_incidence_range : 1-9 / 100 000 Sweden AND has_annual_incidence_average_value : 1.1 AND has_annual_incidence_range : 1-9 / 100 000 Sweden AND has_point_prevalence_average_value : 21.0 AND has_point_prevalence_range : 1-5 / 10 000 United States AND has_point_prevalence_average_value : 11.2 AND has_point_prevalence_range : 1-5 / 10 000 Finland AND has_annual_incidence_average_value : 3.5 AND has_annual_incidence_range : 1-9 / 100 000 Finland AND has_point_prevalence_average_value : 75.3 AND has_point_prevalence_range : 6-9 / 10 000 United States AND has_annual_incidence_average_value : 0.98 AND has_annual_incidence_range : 1-9 / 1 000 000 United Kingdom AND has_point_prevalence_average_value : 11.5 AND has_point_prevalence_range : 1-5 / 10 000 Italy AND has_annual_incidence_average_value : 0.9 AND has_annual_incidence_range : 1-9 / 1 000 000 Ireland AND has_point_prevalence_average_value : 17.6 AND has_point_prevalence_range : 1-5 / 10 000 Europe AND has_point_prevalence_average_value : 27.0 AND has_point_prevalence_range : 1-5 / 10 000 |
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| treeView | ||
| subClassOf |