Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Jump to:
loading...
Preferred Name

Acrodermatitis continua of Hallopeau
Synonyms
Definitions

A rare, genetic, chronic, recurrent, slowly progressive, epidermal disease characterized by small, sterile, pustular eruptions, involving the nails and surrounding skin of the fingers and/or toes, which coalesce and burst, leaving erythematous, atrophic skin where new pustules develop. Onychodystrophy is frequently associated and anonychia and osteolysis are reported in severe cases. Local expansion (to involve the hands, forearms and/or feet) and involvement of mucosal surfaces (e.g. conjunctiva, tongue, urethra) may be observed.
ID

http://www.orpha.net/ORDO/Orphanet_163931
definition

A rare, genetic, chronic, recurrent, slowly progressive, epidermal disease characterized by small, sterile, pustular eruptions, involving the nails and surrounding skin of the fingers and/or toes, which coalesce and burst, leaving erythematous, atrophic skin where new pustules develop. Onychodystrophy is frequently associated and anonychia and osteolysis are reported in severe cases. Local expansion (to involve the hands, forearms and/or feet) and involvement of mucosal surfaces (e.g. conjunctiva, tongue, urethra) may be observed.
definition_citation

Orphanet
expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=163931
hasDbXref

ICD-11:EA90.41

UMLS:C0392439

ICD-10:L40.2
label

Acrodermatitis continua of Hallopeau
notation

ORPHA:163931
part_of

http://www.orpha.net/ORDO/Orphanet_79359

http://www.orpha.net/ORDO/Orphanet_79360
prefixIRI

ORDO:Orphanet_163931
prefLabel

Acrodermatitis continua of Hallopeau
treeView

http://www.orpha.net/ORDO/Orphanet_79359

http://www.orpha.net/ORDO/Orphanet_79360
subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493
Add comment
Add proposal
Delete Subject Author Type Created
No notes to display