Preferred Name |
Anti-neutrophil cytoplasmic antibody-associated vasculitis |
|
Synonyms |
Antineutrophil cytoplasmic antibody-associated vasculitis ANCA-associated vasculitis AAV |
|
ID |
http://www.orpha.net/ORDO/Orphanet_156152 |
|
alternative_term |
Antineutrophil cytoplasmic antibody-associated vasculitis ANCA-associated vasculitis AAV |
|
expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=156152 |
|
hasDbXref |
ICD-11:4A44.A UMLS:C2717865 MeSH:D056648 |
|
label |
Anti-neutrophil cytoplasmic antibody-associated vasculitis |
|
notation |
ORPHA:156152 Clinical group |
|
prefixIRI |
ORDO:Orphanet_156152 |
|
prefLabel |
Anti-neutrophil cytoplasmic antibody-associated vasculitis |
|
present_in |
United States AND has_annual_incidence_average_value : 3.3 AND has_annual_incidence_range : 1-9 / 100 000 Germany AND has_point_prevalence_average_value : 14.9 AND has_point_prevalence_range : 1-5 / 10 000 Europe AND has_point_prevalence_range : 1-5 / 10 000 United States AND has_point_prevalence_average_value : 42.1 AND has_point_prevalence_range : 1-5 / 10 000 |
|
subClassOf |
http://www.orpha.net/ORDO/Orphanet_156146 http://www.orpha.net/ORDO/Orphanet_264973 |