Orphanet Rare Disease Ontology

Last uploaded: July 3, 2024
Preferred Name

Anti-neutrophil cytoplasmic antibody-associated vasculitis

Synonyms

Antineutrophil cytoplasmic antibody-associated vasculitis

ANCA-associated vasculitis

AAV

ID

http://www.orpha.net/ORDO/Orphanet_156152

alternative_term

Antineutrophil cytoplasmic antibody-associated vasculitis

ANCA-associated vasculitis

AAV

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=156152

hasDbXref

ICD-11:4A44.A

UMLS:C2717865

MeSH:D056648

label

Anti-neutrophil cytoplasmic antibody-associated vasculitis

notation

ORPHA:156152

Clinical group

prefixIRI

ORDO:Orphanet_156152

prefLabel

Anti-neutrophil cytoplasmic antibody-associated vasculitis

present_in

United States AND has_annual_incidence_average_value : 3.3 AND has_annual_incidence_range : 1-9 / 100 000

Germany AND has_point_prevalence_average_value : 14.9 AND has_point_prevalence_range : 1-5 / 10 000

Europe AND has_point_prevalence_range : 1-5 / 10 000

United States AND has_point_prevalence_average_value : 42.1 AND has_point_prevalence_range : 1-5 / 10 000

subClassOf

http://www.orpha.net/ORDO/Orphanet_156146

http://www.orpha.net/ORDO/Orphanet_264973

http://www.orpha.net/ORDO/Orphanet_280369

http://www.orpha.net/ORDO/Orphanet_557492

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