Orphanet Rare Disease Ontology

Last uploaded: July 3, 2024
Preferred Name

Semantic dementia
Synonyms

Semantic variant PPA

Semantic primary progressive aphasia

Definitions

Semantic dementia (SD) is a form of frontotemporal dementia (FTD; see this term), characterized by the progressive, amodal and profound loss of semantic knowledge (combination of visual associative agnosia, anomia, surface dyslexia or dysgraphia and disrupted comprehension of word meaning) and behavioral abnormalities, attributable to the degeneration of the anterior temporal lobes.

ID

http://www.orpha.net/ORDO/Orphanet_100069

alternative_term

Semantic variant PPA

Semantic primary progressive aphasia

definition

Semantic dementia (SD) is a form of frontotemporal dementia (FTD; see this term), characterized by the progressive, amodal and profound loss of semantic knowledge (combination of visual associative agnosia, anomia, surface dyslexia or dysgraphia and disrupted comprehension of word meaning) and behavioral abnormalities, attributable to the degeneration of the anterior temporal lobes.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=100069

hasDbXref

ICD-11:6D83

UMLS:C0338462

OMIM:172700

ICD-10:G31.0

OMIM:600274

label

Semantic dementia

notation

ORPHA:100069

part_of

http://www.orpha.net/ORDO/Orphanet_95432

http://www.orpha.net/ORDO/Orphanet_282

prefixIRI

ORDO:Orphanet_100069

prefLabel

Semantic dementia

treeView

http://www.orpha.net/ORDO/Orphanet_95432

http://www.orpha.net/ORDO/Orphanet_282

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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