Preferred Name

Primitive Neuroectodermal Neoplasm
Synonyms
Definitions

A group of malignant tumors of the nervous system that feature primitive cells with elements of neuronal and/or glial differentiation. Use of this term is limited by some authors to central nervous system tumors and others include neoplasms of similar origin which arise extracranially (i.e., NEUROECTODERMAL TUMORS, PRIMITIVE, PERIPHERAL). This term is also occasionally used as a synonym for MEDULLOBLASTOMA. In general, these tumors arise in the first decade of life and tend to be highly malignant (MeSH).

ID

http://uri.neuinfo.org/nif/nifstd/birnlex_12629

acronym

PNET

createdDate

2007-10-05

definingCitation

DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2059

definition

A group of malignant tumors of the nervous system that feature primitive cells with elements of neuronal and/or glial differentiation. Use of this term is limited by some authors to central nervous system tumors and others include neoplasms of similar origin which arise extracranially (i.e., NEUROECTODERMAL TUMORS, PRIMITIVE, PERIPHERAL). This term is also occasionally used as a synonym for MEDULLOBLASTOMA. In general, these tumors arise in the first decade of life and tend to be highly malignant (MeSH).

editorial note

http://uri.neuinfo.org/nif/nifstd/readable/uncurated

hasBirnlexCurator

http://uri.neuinfo.org/nif/nifstd/readable/Bill_Bug

hasCurationStatus

http://uri.neuinfo.org/nif/nifstd/readable/uncurated

hasDefinitionSource

http://uri.neuinfo.org/nif/nifstd/readable/MeSH_defSource

hasExternalSource

http://uri.neuinfo.org/nif/nifstd/readable/MeSH

label

Primitive Neuroectodermal Neoplasm

MeshUid

D018242

modifiedDate

2007-10-05

note

A group of malignant tumors of the nervous system that feature primitive cells with elements of neuronal and/or glial differentiation. Use of this term is limited by some authors to central nervous system tumors and others include neoplasms of similar origin which arise extracranially (i.e., NEUROECTODERMAL TUMORS, PRIMITIVE, PERIPHERAL). This term is also occasionally used as a synonym for MEDULLOBLASTOMA. In general, these tumors arise in the first decade of life and tend to be highly malignant (MeSH).

http://uri.neuinfo.org/nif/nifstd/readable/uncurated

preferred label

Primitive Neuroectodermal Neoplasm

putativeClassExtension

Ependymoblastoma

Spongioblastoma

Medulloepithelioma

synonym

Primitive Neuroepithelial Neoplasm

Primitive Neuroectodermal Tumor

Primitive Neuroepithelial Tumor

usageNote

MeSH includes qualified subtypes.

subClassOf

http://uri.neuinfo.org/nif/nifstd/birnlex_12600

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