Preferred Name |
Glutaryl-CoA Dehydrogenase [Chemical/Ingredient] |
|
Synonyms |
Glutaryl CoA Dehydrogenase |
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ID |
http://purl.bioontology.org/ontology/NDFRT/N0000167933 |
|
altLabel |
Glutaryl CoA Dehydrogenase Glutaryl-CoA Dehydrogenase Glutaryl-Coenzyme A Dehydrogenase |
|
cui |
C0061510 |
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MESH DEFINITION |
A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase. |
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MESH DUI |
D050770 |
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MeSH name |
Glutaryl-CoA Dehydrogenase |
|
MESH UI |
M0074614 |
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NDFRT kind |
INGREDIENT_KIND |
|
notation |
N0000167933 |
|
NUI |
N0000167933 |
|
prefLabel |
Glutaryl-CoA Dehydrogenase [Chemical/Ingredient] |
|
tui |
T116 T126 |
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subClassOf |
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