National Cancer Institute Thesaurus

Last uploaded: February 23, 2024
Preferred Name

Primary Systemic Amyloidosis

Synonyms

Primary Systemic Amyloidosis

Definitions

A plasma cell neoplasm that secretes an abnormal immunoglobulin, which deposits in various tissues and forms a beta-pleated sheet structure that binds Congo red dye with characteristic birefringence. The sites of involvement include heart, liver, kidney, gut, tongue, nerves, and bone. (WHO, 2001)

ID

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C8299

code

C8299

Concept_In_Subset

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C116977

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C118168

Contributing_Source

CTRP

DEFINITION

A plasma cell neoplasm that secretes an abnormal immunoglobulin, which deposits in various tissues and forms a beta-pleated sheet structure that binds Congo red dye with characteristic birefringence. The sites of involvement include heart, liver, kidney, gut, tongue, nerves, and bone. (WHO, 2001)

Display_Name

Primary Systemic Amyloidosis

FULL_SYN

Primary Systemic Amyloidosis

label

Primary Systemic Amyloidosis

Legacy Concept Name

Primary_Systemic_Amyloidosis

Neoplastic_Status

Undetermined

Preferred_Name

Primary Systemic Amyloidosis

prefixIRI

Thesaurus:C8299

Semantic_Type

Neoplastic Process

UMLS_CUI

C0268380

subClassOf

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3819

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