Preferred Name |
Primary Systemic Amyloidosis |
|
Synonyms |
Primary Systemic Amyloidosis |
|
Definitions |
A plasma cell neoplasm that secretes an abnormal immunoglobulin, which deposits in various tissues and forms a beta-pleated sheet structure that binds Congo red dye with characteristic birefringence. The sites of involvement include heart, liver, kidney, gut, tongue, nerves, and bone. (WHO, 2001) |
|
ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C8299 |
|
code |
C8299 |
|
Concept_In_Subset | ||
Contributing_Source |
CTRP |
|
DEFINITION |
A plasma cell neoplasm that secretes an abnormal immunoglobulin, which deposits in various tissues and forms a beta-pleated sheet structure that binds Congo red dye with characteristic birefringence. The sites of involvement include heart, liver, kidney, gut, tongue, nerves, and bone. (WHO, 2001) |
|
Display_Name |
Primary Systemic Amyloidosis |
|
FULL_SYN |
Primary Systemic Amyloidosis |
|
label |
Primary Systemic Amyloidosis |
|
Legacy Concept Name |
Primary_Systemic_Amyloidosis |
|
Neoplastic_Status |
Undetermined |
|
Preferred_Name |
Primary Systemic Amyloidosis |
|
prefixIRI |
Thesaurus:C8299 |
|
Semantic_Type |
Neoplastic Process |
|
UMLS_CUI |
C0268380 |
|
subClassOf |