Preferred Name |
Hand-Schuller-Christian Disease |
|
Synonyms |
Hand-Schuller-Christian Disease Multifocal Unisystem Langerhans Cell Histiocytosis Classic Multifocal Langerhans Cell Histiocytosis Multifocal and unisystemic Langerhans-cell histiocytosis Hand-Schüller-Christian Disease Hand-Schuller-Christian disease |
|
Definitions |
A multifocal, unisystem form of Langerhans-cell histiocytosis. There is involvement of multiple sites in one organ system, most frequently the bone. Patients are usually young children presenting with multiple destructive bone lesions. |
|
ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C6920 |
|
ALT_DEFINITION |
A multifocal, unisystem form of Langerhans-cell histiocytosis. There is involvement of multiple sites in one organ system, most frequently the bone. Patients are usually young children presenting with multiple destructive bone lesions. |
|
code |
C6920 |
|
Concept_In_Subset |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C157711 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C156952 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C90259 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C156966 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C118467 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193248 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C126659 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C132009 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193231 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193006 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C158520 |
|
Contributing_Source |
CPTAC GDC NICHD mCode |
|
DEFINITION |
A multifocal, unisystem form of Langerhans-cell histiocytosis. There is involvement of multiple sites in one organ system, most frequently the bone. Patients are usually young children presenting with multiple destructive bone lesions. |
|
FULL_SYN |
Hand-Schuller-Christian Disease Multifocal Unisystem Langerhans Cell Histiocytosis Classic Multifocal Langerhans Cell Histiocytosis Multifocal and unisystemic Langerhans-cell histiocytosis Hand-Schüller-Christian Disease Hand-Schuller-Christian disease |
|
ICD-O-3_Code |
9753/1 |
|
Is_Value_For_GDC_Property | ||
label |
Hand-Schuller-Christian Disease |
|
Legacy Concept Name |
Hand-Schuller-Christian_Disease |
|
Maps_To |
Multifocal and unisystemic Langerhans-cell histiocytosis Hand-Schuller-Christian disease 9751/3 |
|
Neoplastic_Status |
Undetermined |
|
Preferred_Name |
Hand-Schuller-Christian Disease |
|
prefixIRI |
Thesaurus:C6920 |
|
Semantic_Type |
Neoplastic Process |
|
UMLS_CUI |
C0268205 |
|
subClassOf |