loading...| Preferred Name |
Myofibromatosis |
|
| Synonyms |
Infantile Hemangiopericytoma Multicentric Myofibromatosis Infantile myofibromatosis Myofibromatosis Infantile Myofibromatosis |
|
| Definitions |
A benign, multifocal, nodular and well-circumscribed neoplasm usually seen as a congenital neoplasm or in the first year of life. It is characterized by a biphasic growth pattern and is composed of small, undifferentiated mesenchymal cells associated with branching thin-walled vessels and more mature neoplastic spindle cells with abundant eosinophilic cytoplasm in a collagenous stroma. |
|
| ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3742 |
|
| code |
C3742 |
|
| Concept_In_Subset |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C157711 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168661 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168656 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168662 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168658 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168655 |
|
| Contributing_Source |
GDC |
|
| DEFINITION |
A benign, multifocal, nodular and well-circumscribed neoplasm usually seen as a congenital neoplasm or in the first year of life. It is characterized by a biphasic growth pattern and is composed of small, undifferentiated mesenchymal cells associated with branching thin-walled vessels and more mature neoplastic spindle cells with abundant eosinophilic cytoplasm in a collagenous stroma. |
|
| FULL_SYN |
Infantile Hemangiopericytoma Multicentric Myofibromatosis Infantile myofibromatosis Myofibromatosis Infantile Myofibromatosis |
|
| ICD-O-3_Code |
8824/1 |
|
| Is_Value_For_GDC_Property | ||
| label |
Myofibromatosis |
|
| Legacy Concept Name |
Myofibromatosis |
|
| Maps_To |
Infantile myofibromatosis Myofibromatosis 8824/1 |
|
| Neoplastic_Status |
Benign |
|
| Preferred_Name |
Myofibromatosis |
|
| prefixIRI |
Thesaurus:C3742 |
|
| Related_To_Genetic_Biomarker | ||
| Semantic_Type |
Neoplastic Process |
|
| UMLS_CUI |
C0206648 |
|
| subClassOf |