loading...| Preferred Name |
Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor |
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| Synonyms |
Ewing sarcoma family of tumors Ewing's Family of Tumours Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor Ewing Family of Tumors Ewing sarcoma/Peripheral PNET Tumors of the Ewing's Family Ewing's Family of Tumors Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor Tumors of Ewing's Family Ewing sarcoma/Peripheral primitive neuroectodermal tumor EFTs |
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| Definitions |
A spectrum of malignant tumors, affecting mostly males under age 20, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. These tumors may occur in the soft tissues or the bones. Pain and the presence of a mass are the most common clinical symptoms. |
|
| ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C27291 |
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| ALT_DEFINITION |
A group of cancers that includes Ewing tumor of bone (ETB or Ewing sarcoma of bone), extraosseous Ewing (EOE) tumors, primitive neuroectodermal tumors (PNET or peripheral neuroepithelioma), and Askin tumors (PNET of the chest wall). These tumors all come from the same type of stem cell. |
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| code |
C27291 |
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| Concept_In_Subset |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C116977 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C192842 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C126659 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C118168 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C165258 |
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| Contributing_Source |
Cellosaurus CTEP CTRP |
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| DEFINITION |
A spectrum of malignant tumors, affecting mostly males under age 20, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. These tumors may occur in the soft tissues or the bones. Pain and the presence of a mass are the most common clinical symptoms. |
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| Display_Name |
Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor |
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| FULL_SYN |
Ewing sarcoma family of tumors Ewing's Family of Tumours Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor Ewing Family of Tumors Ewing sarcoma/Peripheral PNET Tumors of the Ewing's Family Ewing's Family of Tumors Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor Tumors of Ewing's Family Ewing sarcoma/Peripheral primitive neuroectodermal tumor EFTs |
|
| label |
Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor |
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| Legacy Concept Name |
Ewing_s_Sarcoma_Peripheral_Primitive_Neuroectodermal_Tumor |
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| Neoplastic_Status |
Malignant |
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| Preferred_Name |
Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor |
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| prefixIRI |
Thesaurus:C27291 |
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| Semantic_Type |
Neoplastic Process |
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| UMLS_CUI |
C0684337 |
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| subClassOf |