Medical Subject Headings

Last uploaded: January 16, 2025

Id	http://purl.bioontology.org/ontology/MESH/D000077733 http://purl.bioontology.org/ontology/MESH/D000077733
Preferred Name	Immunoglobulin G4-Related Disease
Definitions	A spectrum of systemic autoimmune diseases in which IMMUNOGLOBULIN G4 plays a pathophysiologic role. It can affect multiple organs in highly variable presentations, characterized by inflammatory lesions composed of IgG4-positive PLASMA CELLS, further infiltrated by T helper cells (T-LYMPHOCYTES, HELPER-INDUCER) when linked to progressive FIBROSIS and eventual organ damage.
Synonyms	IgG4-Related Sclerosing Diseases IgG4-RD IgG4 Related Disease IgG4-Related Kidney Diseases Immunoglobulin G4-Related Kidney Disease Immunoglobulin G4 Related Disease IgG4-Related Disease IgG4 Related Systemic Disease Kidney Disease, IgG4-Related IgG4-Related Sclerosing Disease IgG4-Associated Autoimmune Diseases IgG4-Related Kidney Disease Sclerosing Disease, IgG4-Related IgG4-Related Diseases Immunoglobulin G4 Related Sclerosing Disease IgG4 Associated Autoimmune Disease Immunoglobulin G4-Related Sclerosing Disease Immunoglobulin G4 Related Kidney Disease IgG4 Related Sclerosing Disease IgG4 Related Kidney Disease Autoimmune Disease, IgG4-Associated Immunoglobulin G4-Related Diseases IgG4-Associated Autoimmune Disease See more See less
Type	http://www.w3.org/2002/07/owl#Class

definition	A spectrum of systemic autoimmune diseases in which IMMUNOGLOBULIN G4 plays a pathophysiologic role. It can affect multiple organs in highly variable presentations, characterized by inflammatory lesions composed of IgG4-positive PLASMA CELLS, further infiltrated by T helper cells (T-LYMPHOCYTES, HELPER-INDUCER) when linked to progressive FIBROSIS and eventual organ damage.
altLabel	IgG4-Related Sclerosing Diseases IgG4-RD IgG4 Related Disease IgG4-Related Kidney Diseases Immunoglobulin G4-Related Kidney Disease Immunoglobulin G4 Related Disease IgG4-Related Disease IgG4 Related Systemic Disease Kidney Disease, IgG4-Related IgG4-Related Sclerosing Disease IgG4-Associated Autoimmune Diseases IgG4-Related Kidney Disease Sclerosing Disease, IgG4-Related IgG4-Related Diseases Immunoglobulin G4 Related Sclerosing Disease IgG4 Associated Autoimmune Disease Immunoglobulin G4-Related Sclerosing Disease Immunoglobulin G4 Related Kidney Disease IgG4 Related Sclerosing Disease IgG4 Related Kidney Disease Autoimmune Disease, IgG4-Associated Immunoglobulin G4-Related Diseases IgG4-Associated Autoimmune Disease See more See less
prefLabel	Immunoglobulin G4-Related Disease
TH	NLM (2019) NLM (2021)
notation	D000077733
DX	20190101
Machine permutation	2019
MN	C20.111.572
MMR	20200116
AQL	BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI
HN	2019
subClassOf	http://purl.bioontology.org/ontology/MESH/D001327
Semantic type UMLS property	http://purl.bioontology.org/ontology/STY/T047
DC	1
MDA	20180709
Inverse of RO	http://purl.bioontology.org/ontology/MESH/D000081012
type	http://www.w3.org/2002/07/owl#Class
tui	T047
cui	C3203653 C4087124 C5392056
Inverse of AQ	http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000178 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000469 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000209 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000523 http://purl.bioontology.org/ontology/MESH/Q000401 See more See less
TERMUI	T000940965 T000940969 T000940966 T000998461 T000940968 T000940967 T000998459 T000998464 T000998463 See more See less

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