Preferred Name | Frontotemporal Lobar Degeneration | |
Synonyms |
FTLDs Lobar Degenerations, Frontotemporal Degeneration, Frontotemporal Lobar Lobar Degeneration, Frontotemporal Frontotemporal Lobar Degenerations Degenerations, Frontotemporal Lobar FTLD |
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Definitions |
Heterogeneous group of neurodegenerative disorders characterized by frontal and temporal lobe atrophy associated with neuronal loss, gliosis, and dementia. Patients exhibit progressive changes in social, behavioral, and/or language function. Multiple subtypes or forms are recognized based on presence or absence of TAU PROTEIN inclusions. FTLD includes three clinical syndromes: FRONTOTEMPORAL DEMENTIA, semantic dementia, and PRIMARY PROGRESSIVE NONFLUENT APHASIA. |
|
ID |
http://purl.bioontology.org/ontology/MESH/D057174 |
|
altLabel |
FTLDs Lobar Degenerations, Frontotemporal Degeneration, Frontotemporal Lobar Lobar Degeneration, Frontotemporal Frontotemporal Lobar Degenerations Degenerations, Frontotemporal Lobar FTLD |
|
AQL |
BL CF CI CL CO DG DH DI DT EC EH EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH SU TH UR VI |
|
cui |
C0751072 |
|
DC |
1 |
|
definition |
Heterogeneous group of neurodegenerative disorders characterized by frontal and temporal lobe atrophy associated with neuronal loss, gliosis, and dementia. Patients exhibit progressive changes in social, behavioral, and/or language function. Multiple subtypes or forms are recognized based on presence or absence of TAU PROTEIN inclusions. FTLD includes three clinical syndromes: FRONTOTEMPORAL DEMENTIA, semantic dementia, and PRIMARY PROGRESSIVE NONFLUENT APHASIA. |
|
DX |
20100101 |
|
HN |
2010; use DEMENTIA 2000-2009; for SEMANTIC DEMENTIA use DEMENTIA 2000-2009 |
|
Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000178 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000469 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000209 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000652 |
|
Machine permutation |
2010; see DEMENTIA 2000-2009; for SEMANTIC DEMENTIA see DEMENTIA 2000-2009 |
|
Mapped from | ||
MDA |
20090706 |
|
MMR |
20150623 |
|
MN |
C18.452.845.800.300 F03.615.400.380 C10.228.140.380.266 C10.574.950.300 |
|
notation |
D057174 |
|
prefLabel |
Frontotemporal Lobar Degeneration |
|
TERMUI |
T749894 T367222 |
|
TH |
OMIM (2013) NLM (2000) NLM (2010) GHR (2014) |
|
tui |
T048 |
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subClassOf |