Iduronidase
alpha-L-Idosiduronase
An enzyme that hydrolyzes iduronosidic linkages in desulfated dermatan. Deficiency of this enzyme produces Hurler's syndrome. EC 3.2.1.76.
http://purl.bioontology.org/ontology/MESH/D007068
alpha L Idosiduronase
Glycosaminoglycan alpha-L-iduronohydrolase
alpha L Iduronidase
alpha-L-Iduronidase
/defic: consider also MUCOPOLYSACCHARIDOSIS I
AD AE AI AN BI BL CF CH CL CS DE DF EC GE HI IM IP ME PD PH PK PO RE SD ST TO TU UL UR
C0020818
1
19910101
D008059
91(75); was see under GLYCOSIDE HYDROLASES 1975-90
http://purl.bioontology.org/ontology/MESH/Q000097
http://purl.bioontology.org/ontology/MESH/Q000096
http://purl.bioontology.org/ontology/MESH/Q000172
http://purl.bioontology.org/ontology/MESH/Q000627
http://purl.bioontology.org/ontology/MESH/Q000648
http://purl.bioontology.org/ontology/MESH/Q000493
http://purl.bioontology.org/ontology/MESH/Q000494
http://purl.bioontology.org/ontology/MESH/Q000276
http://purl.bioontology.org/ontology/MESH/Q000138
http://purl.bioontology.org/ontology/MESH/Q000134
http://purl.bioontology.org/ontology/MESH/Q000266
http://purl.bioontology.org/ontology/MESH/Q000378
http://purl.bioontology.org/ontology/MESH/Q000008
http://purl.bioontology.org/ontology/MESH/Q000009
http://purl.bioontology.org/ontology/MESH/Q000032
http://purl.bioontology.org/ontology/MESH/Q000037
http://purl.bioontology.org/ontology/MESH/Q000191
http://purl.bioontology.org/ontology/MESH/Q000302
http://purl.bioontology.org/ontology/MESH/Q000145
http://purl.bioontology.org/ontology/MESH/Q000592
http://purl.bioontology.org/ontology/MESH/Q000737
http://purl.bioontology.org/ontology/MESH/Q000502
http://purl.bioontology.org/ontology/MESH/Q000506
http://purl.bioontology.org/ontology/MESH/Q000187
http://purl.bioontology.org/ontology/MESH/Q000235
http://purl.bioontology.org/ontology/MESH/Q000633
http://purl.bioontology.org/ontology/MESH/Q000600
http://purl.bioontology.org/ontology/MESH/Q000652
http://purl.bioontology.org/ontology/MESH/Q000528
EC 3.2.1.76
http://purl.bioontology.org/ontology/MESH/D008059
91; was see under GLYCOSIDE HYDROLASES 1975-90
http://purl.bioontology.org/ontology/MESH/C000723131
http://purl.bioontology.org/ontology/MESH/C546866
http://purl.bioontology.org/ontology/MESH/C000615655
19741119
20030709
D08.811.277.450.560
D007068
T021151
T021149
T021150
NLM (1975)
UNK (19XX)
T116
T126
http://purl.bioontology.org/ontology/MESH/D006026