loading...| Preferred Name |
Histiocytosis, Langerhans-Cell |
|
| Synonyms |
Histiocytosis X Disease, Letterer-Siwe |
|
| Definitions |
A group of disorders resulting from the abnormal proliferation of and tissue infiltration by LANGERHANS CELLS which can be detected by their characteristic Birbeck granules (X bodies), or by monoclonal antibody staining for their surface CD1 ANTIGENS. Langerhans-cell granulomatosis can involve a single organ, or can be a systemic disorder. |
|
| ID |
http://purl.bioontology.org/ontology/MESH/D006646 |
|
| altLabel |
Histiocytosis X Letterer-Siwe Disease Pulmonary Histiocytosis X Histiocytosis, Type 2 Hand-Schüller-Christian Disease Cell Histiocytoses, Langerhans Pulmonary Langerhans Cell Granulomatosis Hand Schüller Christian Disease Histiocytosis-X Hand Schüller Christian Syndrome Syndrome, Hand-Schueller-Christian Letterer Siwe Disease Non-Lipid Reticuloendothelioses Cell Granulomatoses, Langerhans Granulomatosis, Langerhans-Cell Histiocytosis, Generalized Disease, Hand-Schueller-Christian Generalized Histiocytosis Histiocytoses, Generalized Histiocytosis, Langerhans Cell Type 2 Histiocytosis Hashimoto-Pritzger Disease Disease, Hand-Schüller-Christian Hand-Schueller-Christian Syndrome Non-Lipid Reticuloendotheliosis Reticuloendothelioses, Non-Lipid Hashimoto Pritzger Disease Granulomatoses, Langerhans Cell Disease, Hashimoto-Pritzger Reticuloendotheliosis, Systemic Aleukemic Cell Histiocytosis, Langerhans Cell Granulomatosis, Langerhans Histiocytosis X, Pulmonary Generalized Histiocytoses Histiocytoses, Type 2 Hand-Schueller-Christian Disease Langerhans Cell Histiocytoses Langerhans Cell Histiocytosis Type 2 Histiocytoses Hand Schueller Christian Syndrome Systemic Aleukemic Reticuloendotheliosis Langerhans-Cell Histiocytosis Granulomatosis, Langerhans Cell Diseases, Hashimoto-Pritzger Langerhans-Cell Granulomatosis Schueller Christian Disease Disease, Schueller-Christian Reticuloendotheliosis, Non-Lipid Systemic Aleukemic Reticuloendothelioses Syndrome, Hand-Schüller-Christian Reticuloendothelioses, Systemic Aleukemic Aleukemic Reticuloendotheliosis, Systemic Langerhans Cell Granulomatosis Hand-Schüller-Christian Syndrome Schueller-Christian Disease Non Lipid Reticuloendotheliosis Langerhans Cell Granulomatosis, Pulmonary Hashimoto-Pritzger Diseases Aleukemic Reticuloendothelioses, Systemic Langerhans Cell Granulomatoses Histiocytoses, Langerhans Cell Hand Schueller Christian Disease Disease, Letterer-Siwe |
|
| AQL |
BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI |
|
| cui |
C5574737 C3661439 C0023381 C0019621 C1455705 |
|
| DC |
1 |
|
| definition |
A group of disorders resulting from the abnormal proliferation of and tissue infiltration by LANGERHANS CELLS which can be detected by their characteristic Birbeck granules (X bodies), or by monoclonal antibody staining for their surface CD1 ANTIGENS. Langerhans-cell granulomatosis can involve a single organ, or can be a systemic disorder. |
|
| DX |
19760101 |
|
| HN |
90(75); was see under RETICULOENDOTHELIOSIS 1966-75; was HISTIOCYTOSIS X 1975-89 |
|
| Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000178 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000469 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000209 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000652 |
|
| Machine permutation |
90; was see under RETICULOENDOTHELIOSIS 1965-75; was HISTIOCYTOSIS X 1975-89 |
|
| Mapped from | ||
| MDA |
19750725 |
|
| MMR |
20230531 |
|
| MN |
C15.604.250.400 C08.381.483.375 |
|
| notation |
D006646 |
|
| OL |
use HISTIOCYTOSIS, LANGERHANS-CELL to search HISTIOCYTOSIS X 1975-89; use RETICULOENDOTHELIOSIS 1966-74 |
|
| prefLabel |
Histiocytosis, Langerhans-Cell |
|
| TERMUI |
T703224 T023616 T020011 T768825 T782968 T020013 T768737 T782967 T705960 T782969 T841870 T018895 T023615 T018896 T811619 T703203 T703225 T020012 T841871 T768826 T020014 |
|
| TH |
OMIM (2013) NLM (2009) NLM (1966) NLM (1990) NLM (1976) NLM (2012) UNK (19XX) GHR (2014) NLM (2011) ORD (2010) |
|
| tui |
T047 T191 |
|
| subClassOf |