loading...| Preferred Name | Glycogen Debranching Enzyme System | |
| Synonyms |
Transfer Glucosidase Debranching Enzyme, Glycogen Enzyme, Glycogen Debranching Transfer-Glucosidase Glycogen Debranching Enzyme |
|
| Definitions |
1,4-alpha-D-Glucan-1,4-alpha-D-glucan 4-alpha-D-glucosyltransferase/dextrin 6 alpha-D-glucanohydrolase. An enzyme system having both 4-alpha-glucanotransferase (EC 2.4.1.25) and amylo-1,6-glucosidase (EC 3.2.1.33) activities. As a transferase it transfers a segment of a 1,4-alpha-D-glucan to a new 4-position in an acceptor, which may be glucose or another 1,4-alpha-D-glucan. As a glucosidase it catalyzes the endohydrolysis of 1,6-alpha-D-glucoside linkages at points of branching in chains of 1,4-linked alpha-D-glucose residues. Amylo-1,6-glucosidase activity is deficient in glycogen storage disease type III. |
|
| ID |
http://purl.bioontology.org/ontology/MESH/D006004 |
|
| altLabel |
Transfer Glucosidase Debranching Enzyme, Glycogen Enzyme, Glycogen Debranching Transfer-Glucosidase Glycogen Debranching Enzyme |
|
| AN |
/defic: consider also GLYCOGEN STORAGE DISEASE TYPE III |
|
| AQL |
AD AE AI AN BI BL CF CH CL CS DE DF EC GE HI IM IP ME PD PH PK PO RE SD ST TO TU UL UR |
|
| cui |
C0017915 C0086358 |
|
| DC |
1 |
|
| definition |
1,4-alpha-D-Glucan-1,4-alpha-D-glucan 4-alpha-D-glucosyltransferase/dextrin 6 alpha-D-glucanohydrolase. An enzyme system having both 4-alpha-glucanotransferase (EC 2.4.1.25) and amylo-1,6-glucosidase (EC 3.2.1.33) activities. As a transferase it transfers a segment of a 1,4-alpha-D-glucan to a new 4-position in an acceptor, which may be glucose or another 1,4-alpha-D-glucan. As a glucosidase it catalyzes the endohydrolysis of 1,6-alpha-D-glucoside linkages at points of branching in chains of 1,4-linked alpha-D-glucose residues. Amylo-1,6-glucosidase activity is deficient in glycogen storage disease type III. |
|
| DX |
19890101 |
|
| FX |
D006010 |
|
| HN |
89(76); was GLYCOGEN DEBRANCHING ENZYME see under GLUCOSYLTRANSFERASES 1976-88 |
|
| Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000096 http://purl.bioontology.org/ontology/MESH/Q000172 http://purl.bioontology.org/ontology/MESH/Q000627 http://purl.bioontology.org/ontology/MESH/Q000648 http://purl.bioontology.org/ontology/MESH/Q000493 http://purl.bioontology.org/ontology/MESH/Q000494 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000138 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000008 http://purl.bioontology.org/ontology/MESH/Q000009 http://purl.bioontology.org/ontology/MESH/Q000032 http://purl.bioontology.org/ontology/MESH/Q000037 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000302 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000592 http://purl.bioontology.org/ontology/MESH/Q000737 http://purl.bioontology.org/ontology/MESH/Q000502 http://purl.bioontology.org/ontology/MESH/Q000506 http://purl.bioontology.org/ontology/MESH/Q000187 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000633 http://purl.bioontology.org/ontology/MESH/Q000600 |
|
| Inverse of RB |
0 |
|
| Inverse of RO | ||
| Machine permutation |
89; was GLYCOGEN DEBRANCHING ENZYME see under GLUCOSYLTRANSFERASES 1976-88 |
|
| Mapped from |
http://purl.bioontology.org/ontology/MESH/C030563 http://purl.bioontology.org/ontology/MESH/C577876 |
|
| MDA |
19750721 |
|
| MMR |
20030709 |
|
| MN |
D08.811.277.450.420.450 D08.811.913.400.450.460.350 |
|
| notation |
D006004 |
|
| OL |
use GLYCOGEN DEBRANCHING ENZYME SYSTEM to search GLYCOGEN DEBRANCHING ENZYME 1976-88 |
|
| prefLabel |
Glycogen Debranching Enzyme System |
|
| TERMUI |
T018237 T018236 T018238 |
|
| TH |
NLM (1976) UNK (19XX) |
|
| tui |
T116 T126 |
|
| subClassOf |