Preferred Name |
adrenal cortex carcinoma |
|
Synonyms |
ACC adrenocortical carcinoma, NOS adrenal cortex carcinoma adrenocortical carcinoma (disease) adrenal cortex cancer adrenal cortex adenocarcinoma adrenal cortical carcinoma adrenocortical cancer carcinoma of adrenal cortex cortical cell carcinoma adenocarcinoma, adrenocortical, malignant cancer of the adrenal cortex neoplasm of adrenal cortex malignant tumour of adrenal cortex adrenal cortical tumors adrenocortical carcinoma adrenal cortical carcinoma (morphologic abnormality) carcinoma, adrenocortical, malignant carcinoma of the adrenal cortex malignant adrenocortical tumor adrenal cortical adenocarcinoma malignant neoplasm of adrenal cortex |
|
Definitions |
A rare, usually large (greater than 5cm), malignant epithelial tumor arising from the adrenal cortical cells. Symptoms are usually related to the excessive production of hormones, and include Cushing's syndrome and virilism in women. Common sites of metastasis include liver, lung, bone, and retroperitoneal lymph nodes. Advanced radiologic procedures have enabled the detection of small tumors, resulting in the improvement of the 5-year survival. |
|
ID |
http://purl.obolibrary.org/obo/MONDO_0006639 |
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closeMatch |
http://identifiers.org/snomedct/127022002 http://identifiers.org/snomedct/189645007 http://identifiers.org/snomedct/363479004 http://linkedlifedata.com/resource/umls/id/C0346402 http://identifiers.org/mesh/D000306 http://identifiers.org/snomedct/93664009 http://linkedlifedata.com/resource/umls/id/C0001618 http://identifiers.org/snomedct/189648009 |
|
conformsTo |
http://purl.obolibrary.org/obo/mondo/patterns/carcinoma.yaml |
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database_cross_reference |
EFO:1000796 DOID:3959 UMLS:C0206686 MedDRA:10001388 Orphanet:1501 SCTID:255035007 ICD10:C74.0 ICDO:8370/3 HP:0006744 GARD:0000558 NCIT:C9325 DOID:660 DOID:3948 ONCOTREE:ACC |
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exactMatch |
http://purl.obolibrary.org/obo/DOID_660 http://www.orpha.net/ORDO/Orphanet_1501 http://identifiers.org/snomedct/255035007 http://purl.obolibrary.org/obo/NCIT_C9325 http://purl.obolibrary.org/obo/DOID_3959 http://purl.obolibrary.org/obo/DOID_3948 http://identifiers.org/mesh/D018268 |
|
excluded from QC check |
http://purl.obolibrary.org/obo/mondo/sparql/single-child-tags.sparql |
|
has exact synonym |
adrenal cortex carcinoma adrenocortical carcinoma (disease) adrenal cortex cancer adrenal cortex adenocarcinoma adrenal cortical carcinoma adrenocortical cancer carcinoma of adrenal cortex cortical cell carcinoma adenocarcinoma, adrenocortical, malignant cancer of the adrenal cortex neoplasm of adrenal cortex malignant tumour of adrenal cortex adrenal cortical tumors adrenocortical carcinoma adrenal cortical carcinoma (morphologic abnormality) carcinoma, adrenocortical, malignant carcinoma of the adrenal cortex malignant adrenocortical tumor adrenal cortical adenocarcinoma malignant neoplasm of adrenal cortex |
|
has related synonym |
ACC adrenocortical carcinoma, NOS |
|
id |
MONDO:0006639 |
|
imported from | ||
in_subset | ||
label |
adrenal cortex carcinoma |
|
notation |
MONDO:0006639 |
|
prefLabel |
adrenal cortex carcinoma |
|
textual definition |
A rare, usually large (greater than 5cm), malignant epithelial tumor arising from the adrenal cortical cells. Symptoms are usually related to the excessive production of hormones, and include Cushing's syndrome and virilism in women. Common sites of metastasis include liver, lung, bone, and retroperitoneal lymph nodes. Advanced radiologic procedures have enabled the detection of small tumors, resulting in the improvement of the 5-year survival. |
|
excluded subClassOf | ||
subClassOf |
http://purl.obolibrary.org/obo/MONDO_0004993 http://purl.obolibrary.org/obo/MONDO_0019748 http://purl.obolibrary.org/obo/MONDO_0021312 http://purl.obolibrary.org/obo/MONDO_0002814 http://purl.obolibrary.org/obo/MONDO_0005086 |