Preferred Name

Primary lymphedema

Synonyms

Malformación troncular linfática

Malformation lymphatique tronculaire

Troncular lymphatic malformation

Malformazione linfatica tronculare

Trunkuläre lymphatische Fehlbildung

ID

http://www.limics.org/hrdo/rdfns#pat_id_11097

ageOfOnset

Erwachsenenalter

Adulte

La edad adulta

Età adulta

Adulthood

Adulthood

Idade adulta

altLabel

Malformación troncular linfática

Malformation lymphatique tronculaire

Troncular lymphatic malformation

Trunkuläre lymphatische Fehlbildung

Malformazione linfatica tronculare

id_Medline

http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=DetailsSearch&Term=(lymphedema%5Bti%5D+OR+lymphedema%5Bmajr%5D)+(humans+OR+patients)+NOT+syndrome

id_OMS

I89.0

id_Orpha

77240

patType

group of phenomes

prefixIRI

hrdo:pat_id_11097

prefLabel

Primary lymphedema

Lymphoedème primaire

Linfedema primário (termo genérico)

Linfedema primario

Primary lymphedema

Linfedema primitivo

prevalence

1-5 / 10 000

1-5 / 10 000

1-5 / 10 000

1-5 / 10 000

1-5 / 10 000

1-5 / 10 000

1-5 / 10 000

subClassOf

http://www.limics.org/hrdo/rdfns#pat_id_11409

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