loading...| Preferred Name | Craniopharyngioma | |
| Synonyms |
Dysodontogenic epithelial tumor Adamantinomatous tumor Adamantinomatous tumour craniopharyngeal duct tumour Dysodontogenic epithelial tumour craniopharyngeal duct tumor cystoma tumour of Rathke's pouch Rathke's pouch tumor craniopharyngioma, benign tumor of Rathke's pouch Rathke's pouch tumour neoplasm of Rathke's pouch craniopharyngioma (WHO grade I) Rathke's pouch neoplasm Rathke pouch tumor craniopharyngioma (morphologic abnormality) craniopharyngioma Rathke pouch tumour Rathke pouch neoplasm |
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| Definitions |
A benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma. The most significant factor associated with recurrence is the extent of surgical resection, with lesions greater than 5 cm in diameter carrying a markedly worse prognosis. (Adapted from WHO) |
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| ID |
http://www.ebi.ac.uk/efo/EFO_1000209 |
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| closeMatch | ||
| database_cross_reference |
SCTID:189179009 MONDO:0018907 NANDO:2200091 ICDO:9350/1 ICD10:D44.4 Orphanet:54595 GARD:0010486 MedDRA:10011318 UMLS:C0010276 EFO:1000209 MEDGEN:41339 MESH:D003397 DOID:3840 GARD:10486 ICD9:237.0 NCIT:C2964 NORD:1996 |
|
| definition |
A benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma. The most significant factor associated with recurrence is the extent of surgical resection, with lesions greater than 5 cm in diameter carrying a markedly worse prognosis. (Adapted from WHO) |
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| disease has location | ||
| exactMatch |
http://identifiers.org/meddra/10011318 http://purl.obolibrary.org/obo/EFO_1000209 http://linkedlifedata.com/resource/umls/id/C0010276 http://purl.obolibrary.org/obo/NCIT_C2964 http://purl.obolibrary.org/obo/Orphanet_54595 http://purl.obolibrary.org/obo/DOID_3840 http://identifiers.org/medgen/41339 |
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| has_exact_synonym |
tumour of Rathke's pouch Rathke's pouch tumor craniopharyngioma, benign tumor of Rathke's pouch Rathke's pouch tumour neoplasm of Rathke's pouch craniopharyngioma (WHO grade I) Rathke's pouch neoplasm Rathke pouch tumor craniopharyngioma (morphologic abnormality) craniopharyngioma Rathke pouch tumour Rathke pouch neoplasm cystoma |
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| has_related_synonym |
Dysodontogenic epithelial tumor Adamantinomatous tumor Adamantinomatous tumour craniopharyngeal duct tumour Dysodontogenic epithelial tumour craniopharyngeal duct tumor cystoma |
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| id |
EFO:1000209 |
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| in_subset |
http://purl.obolibrary.org/obo/mondo/mondo-base#rare http://purl.obolibrary.org/obo/mondo#ordo_disease http://purl.obolibrary.org/obo/mondo/mondo-base#otar http://purl.obolibrary.org/obo/mondo/mondo-base#gard_rare http://purl.obolibrary.org/obo/mondo/mondo-base#orphanet_rare http://purl.obolibrary.org/obo/mondo/mondo-base#nord_rare http://purl.obolibrary.org/obo/mondo/mondo-base#ordo_disorder |
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| label |
Craniopharyngioma |
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| notation |
EFO:1000209 |
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| preferred label |
Craniopharyngioma |
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| prefLabel |
Craniopharyngioma |
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| subClassOf |
http://purl.obolibrary.org/obo/MONDO_0023369 http://purl.obolibrary.org/obo/MONDO_0036976 http://purl.obolibrary.org/obo/MONDO_0002532 http://purl.obolibrary.org/obo/MONDO_0000631 |
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| excluded_subClassOf |