Experimental Factor Ontology

Last uploaded: July 4, 2024
Preferred Name

IgA pemphigus

Synonyms

immunoglobulin A (IgA) pemphigus

immunoglobulin A mediated pemphigus

subcorneal pustular dermatosis and monoclonal IgA

immunoglobulin A (IgA)-mediated pemphigus

immunoglobulin A pemphigus

Definitions

Immunoglobulin A (IgA) pemphigus is a group of newly characterized immune-mediated intraepidermal blistering skin diseases. Unlike typical immunoglobulin G (IgG)–mediated pemphigus, IgA pemphigus is characterized by tissue-bound and circulating IgA autoantibodies that target the desmosomal proteins of the epidermis [ https://emedicine.medscape.com/article/1063776-overview ]

ID

http://www.ebi.ac.uk/efo/EFO_0008604

definition

Immunoglobulin A (IgA) pemphigus is a group of newly characterized immune-mediated intraepidermal blistering skin diseases. Unlike typical immunoglobulin G (IgG)–mediated pemphigus, IgA pemphigus is characterized by tissue-bound and circulating IgA autoantibodies that target the desmosomal proteins of the epidermis [ https://emedicine.medscape.com/article/1063776-overview ]

definition_citation

https://emedicine.medscape.com/article/1063776-overview

has_exact_synonym

immunoglobulin A (IgA) pemphigus

immunoglobulin A mediated pemphigus

subcorneal pustular dermatosis and monoclonal IgA

immunoglobulin A (IgA)-mediated pemphigus

immunoglobulin A pemphigus

label

IgA pemphigus

preferred label

IgA pemphigus

prefixIRI

efo1:EFO_0008604

prefLabel

IgA pemphigus

subClassOf

http://www.ebi.ac.uk/efo/EFO_1000749

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