Preferred Name | idiopathic pulmonary fibrosis | |
Synonyms |
interstitial pneumonitis, usual fibrosing alveolitis Hamman-rich disease familial idiopathic pulmonary fibrosis pulmonary fibrosis, idiopathic fibrosing alveolitis, cryptogenic IPF fibrocystic pulmonary dysplasia idiopathic pulmonary fibrosis, familial cryptogenic fibrosing alveolitis idiopathic pulmonary fibrosis usual interstitial pneumonia CFA UIP |
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Definitions |
Idiopathic pulmonary fibrosis (IPF) is a nonneoplastic pulmonary disease that is characterized by the formation of scar tissue within the lungs in the absence of any known cause. |
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ID |
http://www.ebi.ac.uk/efo/EFO_0000768 |
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closeMatch |
http://identifiers.org/snomedct/237121003 http://identifiers.org/snomedct/700250006 http://identifiers.org/snomedct/233721005 http://identifiers.org/snomedct/426437004 http://purl.obolibrary.org/obo/NCIT_C35715 |
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database_cross_reference |
DOID:0050156 NCIT:C35716 ICD10:J84.112 COHD:45763750 SCTID:196125002 ICD10:J84.1 MedDRA:10021240 Orphanet:2032 GARD:0008609 ICD9:516.31 MESH:D054990 OMIM:178500 EFO:0000768 |
|
definition |
Idiopathic pulmonary fibrosis (IPF) is a nonneoplastic pulmonary disease that is characterized by the formation of scar tissue within the lungs in the absence of any known cause. |
|
exactMatch |
http://purl.obolibrary.org/obo/DOID_0050156 http://identifiers.org/mesh/D054990 http://purl.obolibrary.org/obo/NCIT_C35716 http://identifiers.org/omim/178500 |
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gwas_trait |
true |
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has_exact_synonym |
fibrocystic pulmonary dysplasia idiopathic pulmonary fibrosis, familial cryptogenic fibrosing alveolitis idiopathic pulmonary fibrosis usual interstitial pneumonia CFA UIP |
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has_related_synonym |
interstitial pneumonitis, usual fibrosing alveolitis Hamman-rich disease familial idiopathic pulmonary fibrosis pulmonary fibrosis, idiopathic fibrosing alveolitis, cryptogenic IPF |
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in_subset | ||
label |
idiopathic pulmonary fibrosis |
|
preferred label |
idiopathic pulmonary fibrosis |
|
prefixIRI |
efo:EFO_0000768 |
|
prefLabel |
idiopathic pulmonary fibrosis |
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see also |
https://rarediseases.info.nih.gov/diseases/8609/idiopathic-pulmonary-fibrosis |
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subClassOf |