Preferred Name | atypical chronic myeloid leukemia, BCR-ABL1 negative | |
Synonyms |
subacute myelogenous leukaemia subacute granulocytic leukaemia subacute granulocytic leukemia subacute myeloid leukaemia atypical chronic myeloid leukemia, BCR-ABL1 Negative atypical chronic myeloid leukemia atypical chronic myeloid leukaemia subacute myeloid leukemia subacute myelogenous leukemia atypical chronic myeloid leukaemia BCR-ABL1 negative atypical CML atypical chronic myeloid leukemia BCR-ABL1 negative aCML |
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Definitions |
A myelodysplastic/myeloproliferative neoplasm characterized by the principal involvement of the neutrophil series with leukocytosis and multilineage dysplasia. The neoplastic cells do not have a Philadelphia chromosome or the BCR/ABL fusion gene. (WHO, 2001) |
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ID |
http://purl.obolibrary.org/obo/MONDO_0004653 |
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closeMatch | ||
database_cross_reference |
UMLS:C1292772 Orphanet:98824 MedDRA:10054651 MEDGEN:266233 SCTID:277589003 ICDO:9876/3 DOID:0060597 icd11.foundation:331838766 DOID:8747 GARD:19583 NCIT:C3519 |
|
definition |
A myelodysplastic/myeloproliferative neoplasm characterized by the principal involvement of the neutrophil series with leukocytosis and multilineage dysplasia. The neoplastic cells do not have a Philadelphia chromosome or the BCR/ABL fusion gene. (WHO, 2001) |
|
exactMatch |
http://identifiers.org/snomedct/277589003 http://purl.obolibrary.org/obo/NCIT_C3519 http://identifiers.org/medgen/266233 http://www.orpha.net/ORDO/Orphanet_98824 |
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has_exact_synonym |
subacute myelogenous leukaemia subacute granulocytic leukaemia subacute granulocytic leukemia subacute myeloid leukaemia atypical chronic myeloid leukemia, BCR-ABL1 Negative atypical chronic myeloid leukemia atypical chronic myeloid leukaemia subacute myeloid leukemia subacute myelogenous leukemia atypical chronic myeloid leukaemia BCR-ABL1 negative atypical CML atypical chronic myeloid leukemia BCR-ABL1 negative aCML |
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IAO_0000233 | ||
id |
MONDO:0004653 |
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in_subset |
http://purl.obolibrary.org/obo/mondo#ordo_disorder http://purl.obolibrary.org/obo/mondo#rare http://purl.obolibrary.org/obo/mondo#nord_rare |
|
label |
atypical chronic myeloid leukemia, BCR-ABL1 negative |
|
notation |
MONDO:0004653 |
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preferred label |
atypical chronic myeloid leukemia, BCR-ABL1 negative |
|
prefLabel |
atypical chronic myeloid leukemia, BCR-ABL1 negative |
|
subClassOf |
http://purl.obolibrary.org/obo/MONDO_0004643 |