loading...| Preferred Name |
Ewing sarcoma/peripheral primitive neuroectodermal tumor |
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| Synonyms |
Ewing's family of tumours Ewing family of tumors Ewing sarcoma family of tumors Ewing sarcoma/peripheral PNET Ewing's family of tumors tumors of the Ewing's family EFTs tumors of Ewing's family Ewing's sarcoma/peripheral primitive neuroectodermal tumor Ewing sarcoma/peripheral primitive neuroectodermal tumor |
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| Definitions |
A spectrum of malignant tumors, affecting mostly males under age 20, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. These tumors may occur in the soft tissues or the bones. Pain and the presence of a mass are the most common clinical symptoms. |
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| ID |
http://purl.obolibrary.org/obo/MONDO_0021038 |
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| has_exact_synonym |
Ewing's family of tumours Ewing family of tumors Ewing sarcoma family of tumors Ewing sarcoma/peripheral PNET Ewing's family of tumors tumors of the Ewing's family EFTs tumors of Ewing's family Ewing's sarcoma/peripheral primitive neuroectodermal tumor Ewing sarcoma/peripheral primitive neuroectodermal tumor |
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| label |
Ewing sarcoma/peripheral primitive neuroectodermal tumor |
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| prefixIRI |
MONDO:0021038 |
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| prefLabel |
Ewing sarcoma/peripheral primitive neuroectodermal tumor |
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| textual definition |
A spectrum of malignant tumors, affecting mostly males under age 20, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. These tumors may occur in the soft tissues or the bones. Pain and the presence of a mass are the most common clinical symptoms. |
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| subClassOf |