loading...| Preferred Name |
hand-Schuller-Christian disease |
|
| Synonyms |
hand-Schuller-Christian disease multifocal eosinophilic granuloma hand-SChüller-Christian disease chronic multifocal Langerhans cell histiocytosis classic multifocal Langerhans cell histiocytosis multifocal Unisystem Langerhans cell histiocytosis |
|
| Definitions |
A multifocal, unisystem form of Langerhans-cell histiocytosis. There is involvement of multiple sites in one organ system, most frequently the bone. Patients are usually young children presenting with multiple destructive bone lesions. |
|
| ID |
http://purl.obolibrary.org/obo/MONDO_0020519 |
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| altLabel |
hand-Schuller-Christian disease multifocal eosinophilic granuloma hand-SChüller-Christian disease chronic multifocal Langerhans cell histiocytosis classic multifocal Langerhans cell histiocytosis multifocal Unisystem Langerhans cell histiocytosis |
|
| definition |
A multifocal, unisystem form of Langerhans-cell histiocytosis. There is involvement of multiple sites in one organ system, most frequently the bone. Patients are usually young children presenting with multiple destructive bone lesions. |
|
| has_exact_synonym |
hand-Schuller-Christian disease multifocal eosinophilic granuloma hand-SChüller-Christian disease chronic multifocal Langerhans cell histiocytosis classic multifocal Langerhans cell histiocytosis multifocal Unisystem Langerhans cell histiocytosis |
|
| label |
hand-Schuller-Christian disease |
|
| prefixIRI |
MONDO:0020519 |
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| prefLabel |
hand-Schuller-Christian disease |
|
| textual definition |
A multifocal, unisystem form of Langerhans-cell histiocytosis. There is involvement of multiple sites in one organ system, most frequently the bone. Patients are usually young children presenting with multiple destructive bone lesions. |
|
| subClassOf |