Digital medicine Outcomes Value Set (DOVeS) Ontology

Last uploaded: December 13, 2023
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Preferred Name

kaposiform lymphangiomatosis
Synonyms

KLA
Definitions

A generalized lymphatic anomaly characterized by kaposiform spindled lymphatic endothelial cells. Despite the histological similarity between KHE and KLA, the clinical and imaging features are distinctive. KHE-spectrum lesions are unifocal vascular tumors, except in rare reports of multifocal disease. KHE typically presents in early infancy with a characteristic purpuric, cutaneous lesion[PMID:24252784]
ID

http://purl.obolibrary.org/obo/MONDO_0018736
comment

Despite the histological similarity between KHE and KLA, the clinical and imaging features are distinctive. KHE-spectrum lesions are unifocal vascular tumors, except in rare reports of multifocal disease. KHE typically presents in early infancy with a characteristic purpuric, cutaneous lesion[PMID:24252784]
altLabel

KLA
definition

A generalized lymphatic anomaly characterized by kaposiform spindled lymphatic endothelial cells.

Despite the histological similarity between KHE and KLA, the clinical and imaging features are distinctive. KHE-spectrum lesions are unifocal vascular tumors, except in rare reports of multifocal disease. KHE typically presents in early infancy with a characteristic purpuric, cutaneous lesion[PMID:24252784]
disease shares features of

http://purl.obolibrary.org/obo/MONDO_0016236
has characteristic

http://purl.obolibrary.org/obo/MONDO_0021136
has_broad_synonym

KLA
label

kaposiform lymphangiomatosis
prefixIRI

MONDO:0018736
prefLabel

kaposiform lymphangiomatosis
textual definition

A generalized lymphatic anomaly characterized by kaposiform spindled lymphatic endothelial cells.
subClassOf

http://purl.obolibrary.org/obo/MONDO_0024296
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