loading...| Preferred Name |
primary systemic amyloidosis |
|
| Synonyms |
systemic Immunoglobulin Light chain amyloidosis systemic amyloidosis systemic AL amyloidosis |
|
| Definitions |
Primary systemic amyloidosis (PSA) is a form of AL amyloidosis caused by the aggregation and deposition of insoluble amyloid fibrils derived from misfolded monoclonal immunoglobulin light chains usually produced by a plasma cell tumor and characterized by multiple organ involvement. |
|
| ID |
http://purl.obolibrary.org/obo/MONDO_0017816 |
|
| has_exact_synonym |
systemic Immunoglobulin Light chain amyloidosis systemic amyloidosis systemic AL amyloidosis |
|
| label |
primary systemic amyloidosis |
|
| prefixIRI |
MONDO:0017816 |
|
| prefLabel |
primary systemic amyloidosis |
|
| textual definition |
Primary systemic amyloidosis (PSA) is a form of AL amyloidosis caused by the aggregation and deposition of insoluble amyloid fibrils derived from misfolded monoclonal immunoglobulin light chains usually produced by a plasma cell tumor and characterized by multiple organ involvement. |
|
| subClassOf |