Preferred Name |
immunoglobulin light chain amyloidosis |
|
Synonyms |
AL amyloidosis Primary systemic amyloidosis Light chain amyloidosis Primary systemic AL amyloidosis Primary AL amyloidosis Amyloidosis primary systemic Systemic AL amyloidsis |
|
Definitions |
An amyloidosis that is characterized by misfolded and aggregated amyloidogenic immunoglobulin light chains produced by marrow clonal plasma cells. |
|
ID |
http://purl.obolibrary.org/obo/DOID_0080933 |
|
database_cross_reference |
ICD10CM:E85.81 MESH:D000075363 |
|
definition |
An amyloidosis that is characterized by misfolded and aggregated amyloidogenic immunoglobulin light chains produced by marrow clonal plasma cells. |
|
disease has basis in | ||
disease has location |
http://purl.obolibrary.org/obo/UBERON_0001021 http://purl.obolibrary.org/obo/UBERON_0000948 |
|
has exact synonym |
AL amyloidosis Primary systemic amyloidosis Light chain amyloidosis Primary systemic AL amyloidosis Primary AL amyloidosis Amyloidosis primary systemic Systemic AL amyloidsis |
|
has_obo_namespace |
disease_ontology |
|
id |
DOID:0080933 |
|
label |
immunoglobulin light chain amyloidosis |
|
notation |
DOID:0080933 |
|
prefLabel |
immunoglobulin light chain amyloidosis |
|
subClassOf |
http://purl.obolibrary.org/obo/DOID_9120 http://purl.obolibrary.org/obo/DOID_655 http://purl.obolibrary.org/obo/DOID_409 |