Preferred Name |
Primary Systemic Amyloidosis |
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Synonyms |
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ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Primary_Systemic_Amyloidosis |
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DEFINITION |
A plasma cell neoplasm that secretes an abnormal immunoglobulin, which deposits in various tissues and forms a beta-pleated sheet structure that binds Congo red dye with characteristic birefringence. The sites of involvement include heart, liver, kidney, gut, tongue, nerves, and bone. (WHO, 2001) |
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FULL_SYN |
Systemic Amyloidosis |
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isDefinedBy |
A plasma cell neoplasm that secretes an abnormal immunoglobulin, which deposits in various tissues and forms a beta-pleated sheet structure that binds Congo red dye with characteristic birefringence. The sites of involvement include heart, liver, kidney, gut, tongue, nerves, and bone. (WHO, 2001) |
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label |
Primary Systemic Amyloidosis |
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prefixIRI |
Thesaurus:Primary_Systemic_Amyloidosis |
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prefLabel |
Primary Systemic Amyloidosis |
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Synonym |
Systemic Amyloidosis |
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subClassOf |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Primary_Amyloidosis |