Id http://purl.bioontology.org/ontology/CSP/1849-9492
http://purl.bioontology.org/ontology/CSP/1849-9492
Preferred Name

arginosuccinate synthetase deficiency

Definitions
autosomal recessive aminoacidopathy characterized by marked elevation in plasma and urine levels of citrulline, with hyperammonemia and sometimes secondary oroticaciduria; clinical findings include mental retardation and neurologic abnormalities.
Synonyms
ASS deficiency
citrullinemia
citrullinuria
Type http://www.w3.org/2002/07/owl#Class
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