Id http://purl.bioontology.org/ontology/CSP/1849-5536
http://purl.bioontology.org/ontology/CSP/1849-5536
Preferred Name

Krabbe's disease

Definitions
inherited, demyelinating, human lipid storage disease caused by a deficiency of galactosylceramidase; manifestations include convulsions, quadriplegia, blindness, deafness, and mental retardation.
Synonyms
Krabbe's leukodystrophy
globoid cell leukodystrophy
galactosylceramide lipidosis
beta galactocerebrosidase deficiency
Type http://www.w3.org/2002/07/owl#Class
Delete Subject Author Type Created
No notes to display