Id http://purl.bioontology.org/ontology/CSP/1849-1120
http://purl.bioontology.org/ontology/CSP/1849-1120
Preferred Name

methylmalonic aciduria

Definitions
autosomal recessive aminoacidopathy characterized by an excess of methylmalonic acid in the blood and urine, with metabolic ketoacidosis, hyperglycinemia, hyperglycinuria and hyperammonemia; results from defects that cause deficiencies of methylmalonyl-CoA mutase.
Synonyms
methylmalonic acidemia
methylmalonyl coA mutase deficiency
Type http://www.w3.org/2002/07/owl#Class
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