loading...| Preferred Name | dermatitis herpetiformis | |
| Synonyms |
Durhing-Brocq disease Duhring's disease dermatitis herpetiformis dermatosis herpetiformis DH |
|
| Definitions |
Dermatitis herpetiformis (DH) is a chronic autoimmune subepidermal bullous disease characterized by grouped pruritic lesions such as papules, urticarial plaques, erythema, and herpetiform vesiculae, with a predominantly symmetrical distribution on extensor surfaces of the elbows (90%), knees (30%), shoulders, buttocks, sacral region, and face of children and adults. Erosions, excoriations and hyperpigmentation usually follow. DH may also appear as a consequence of gluten intolerance. A chronic blistering skin condition, characterised by blisters filled with a watery fluid. Despite its name, DH is neither related to nor caused by herpes virus: the name means that it is a skin inflammation having an appearance similar to herpes. |
|
| ID |
http://www.ebi.ac.uk/efo/EFO_1000684 |
|
| database_cross_reference |
MONDO:0015614 MEDGEN:8327 icd11.foundation:286313127 Orphanet:1656 NCIT:C26742 UMLS:C0011608 ICD10CM:L13.0 Wikipedia:Dermatitis_herpetiformis MESH:D003874 SCTID:111196000 MedDRA:10012468 DOID:8505 GARD:10075 ICD9:694.0 |
|
| definition |
Dermatitis herpetiformis (DH) is a chronic autoimmune subepidermal bullous disease characterized by grouped pruritic lesions such as papules, urticarial plaques, erythema, and herpetiform vesiculae, with a predominantly symmetrical distribution on extensor surfaces of the elbows (90%), knees (30%), shoulders, buttocks, sacral region, and face of children and adults. Erosions, excoriations and hyperpigmentation usually follow. DH may also appear as a consequence of gluten intolerance. A chronic blistering skin condition, characterised by blisters filled with a watery fluid. Despite its name, DH is neither related to nor caused by herpes virus: the name means that it is a skin inflammation having an appearance similar to herpes. |
|
| has_exact_synonym |
Durhing-Brocq disease Duhring's disease dermatitis herpetiformis dermatosis herpetiformis DH |
|
| id |
EFO:1000684 |
|
| in_subset |
http://purl.obolibrary.org/obo/mondo/mondo-base#rare http://purl.obolibrary.org/obo/mondo/mondo-base#otar http://purl.obolibrary.org/obo/mondo/mondo-base#gard_rare http://purl.obolibrary.org/obo/mondo/mondo-base#orphanet_rare http://purl.obolibrary.org/obo/mondo/mondo-base#ordo_disorder |
|
| label |
dermatitis herpetiformis |
|
| notation |
EFO:1000684 |
|
| preferred label |
dermatitis herpetiformis |
|
| prefLabel |
dermatitis herpetiformis |
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| skos_closeMatch | ||
| skos_exactMatch |
http://purl.obolibrary.org/obo/NCIT_C26742 http://purl.bioontology.org/ontology/ICD10CM/L13.0 http://purl.obolibrary.org/obo/Orphanet_1656 http://identifiers.org/snomedct/111196000 http://identifiers.org/mesh/D003874 http://linkedlifedata.com/resource/umls/id/C0011608 http://purl.obolibrary.org/obo/EFO_1000684 http://purl.obolibrary.org/obo/mondo/sources/icd11foundation/286313127 |
|
| term editor |
Sirarat Sarntivijai |
|
| subClassOf |