loading...| Preferred Name | epithelioid sarcoma | |
| Synonyms |
epithelioid sarcoma epithelioid cell sarcoma ES |
|
| Definitions |
An aggressive malignant neoplasm of uncertain differentiation, characterized by the presence of epithelioid cells forming nodular patterns. The nodules often undergo central necrosis, resulting in a pseudogranulomatous growth pattern. It usually occurs in young adults. The most common sites of involvement are the extremities (distal-type epithelioid sarcoma), and less frequently the pelvis, perineum, and genital organs (proximal-type epithelioid sarcoma). |
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| ID |
http://purl.obolibrary.org/obo/MONDO_0017387 |
|
| database_cross_reference |
UMLS:C0205944 MEDGEN:104753 ONCOTREE:EPIS MedDRA:10015099 ICDO:8804/3 Orphanet:293202 DOID:6193 GARD:10181 NCIT:C3714 |
|
| definition |
An aggressive malignant neoplasm of uncertain differentiation, characterized by the presence of epithelioid cells forming nodular patterns. The nodules often undergo central necrosis, resulting in a pseudogranulomatous growth pattern. It usually occurs in young adults. The most common sites of involvement are the extremities (distal-type epithelioid sarcoma), and less frequently the pelvis, perineum, and genital organs (proximal-type epithelioid sarcoma). |
|
| has_exact_synonym |
epithelioid sarcoma epithelioid cell sarcoma ES |
|
| id |
MONDO:0017387 |
|
| in_subset |
http://purl.obolibrary.org/obo/mondo/mondo-base#rare http://purl.obolibrary.org/obo/mondo/mondo-base#otar http://purl.obolibrary.org/obo/mondo/mondo-base#gard_rare http://purl.obolibrary.org/obo/mondo/mondo-base#orphanet_rare http://purl.obolibrary.org/obo/mondo/mondo-base#nord_rare http://purl.obolibrary.org/obo/mondo/mondo-base#ordo_disorder |
|
| label |
epithelioid sarcoma |
|
| notation |
MONDO:0017387 |
|
| preferred label |
epithelioid sarcoma |
|
| prefLabel |
epithelioid sarcoma |
|
| see also |
https://rarediseases.info.nih.gov/diseases/10181/epithelioid-sarcoma |
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| skos_closeMatch | ||
| skos_exactMatch |
http://linkedlifedata.com/resource/umls/id/C0205944 http://purl.obolibrary.org/obo/DOID_6193 http://purl.obolibrary.org/obo/NCIT_C3714 |
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| subClassOf |