Preferred Name

Peripheral Primitive Neuroectodermal Neoplasm

Synonyms

Peripheral Primitive Neuroectodermal Tumor|Peripheral Neuroectodermal Tumor|Neuroepithelioma|Extracranial Primitive Neuroectodermal Tumor

ID

http://bioontology.org/projects/ontologies/birnlex#birnlex_12630

abbrev

class_or_indiv

true

definition

A group of highly cellular primitive round cell neoplasms which occur extracranially in soft tissue and bone and are derived from embryonal neural crest cells. These tumors occur primarily in children and adolescents and share a number of characteristics with Ewing's Sarcoma ( SARCOMA, EWING'S). They may arise from the chest wall, skin, orbit, kidney, and other structures and tend to be locally invasive or metastasize, although relatively benign forms may occur. Characteristic histologic features include a tendency to form Homer-Wright rosettes and to stain positively with neuron-specific enolase and vimentin (MeSH).

external_id_urls

http://www.nlm.nih.gov/cgi/mesh/2008/MB_cgi?field=uid&term=D018241

external_ids

meshUID:D018241

label

Peripheral Primitive Neuroectodermal Neoplasm

mod_date

2007-10-05

preferred_label

Peripheral Primitive Neuroectodermal Neoplasm

prefixIRI

birnlex_12630

retired

false

synonyms

Peripheral Primitive Neuroectodermal Tumor|Peripheral Neuroectodermal Tumor|Neuroepithelioma|Extracranial Primitive Neuroectodermal Tumor

subClassOf

http://bioontology.org/projects/ontologies/birnlex#birnlex_12629

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