loading...| Preferred Name |
Primary Systemic Amyloidosis |
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| Synonyms |
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| Definitions |
A plasma cell neoplasm that secretes an abnormal immunoglobulin, which deposits in various tissues and forms a beta-pleated sheet structure that binds Congo red dye with characteristic birefringence. The sites of involvement include heart, liver, kidney, gut, tongue, nerves, and bone. (WHO, 2001) |
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| ID |
http://purl.obolibrary.org/obo/NCIT_C8299 |
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| code |
C8299 |
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| Contributing_Source |
CTRP |
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| definition |
A plasma cell neoplasm that secretes an abnormal immunoglobulin, which deposits in various tissues and forms a beta-pleated sheet structure that binds Congo red dye with characteristic birefringence. The sites of involvement include heart, liver, kidney, gut, tongue, nerves, and bone. (WHO, 2001) |
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| Display_Name |
Primary Systemic Amyloidosis |
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| in_subset | ||
| label |
Primary Systemic Amyloidosis |
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| Legacy Concept Name |
Primary_Systemic_Amyloidosis |
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| Neoplastic_Status |
Malignant |
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| Preferred_Name |
Primary Systemic Amyloidosis |
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| prefixIRI |
NCIT:C8299 |
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| prefLabel |
Primary Systemic Amyloidosis |
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| Semantic_Type |
Neoplastic Process |
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| UMLS_CUI |
C0268380 |
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| subClassOf |