Preferred Name |
Hand-Schuller-Christian Disease |
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Synonyms |
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Definitions |
A multifocal, unisystem form of Langerhans-cell histiocytosis. There is involvement of multiple sites in one organ system, most frequently the bone. Patients are usually young children presenting with multiple destructive bone lesions. |
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ID |
http://purl.obolibrary.org/obo/NCIT_C6920 |
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ALT_DEFINITION |
A multifocal, unisystem form of Langerhans-cell histiocytosis. There is involvement of multiple sites in one organ system, most frequently the bone. Patients are usually young children presenting with multiple destructive bone lesions. |
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code |
C6920 |
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Contributing_Source |
CPTAC GDC NICHD |
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definition |
A multifocal, unisystem form of Langerhans-cell histiocytosis. There is involvement of multiple sites in one organ system, most frequently the bone. Patients are usually young children presenting with multiple destructive bone lesions. |
|
ICD-O-3_Code |
9753/1 |
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in_subset |
http://purl.obolibrary.org/obo/NCIT_C90259 http://purl.obolibrary.org/obo/NCIT_C158520 http://purl.obolibrary.org/obo/NCIT_C177537 http://purl.obolibrary.org/obo/NCIT_C156952 http://purl.obolibrary.org/obo/NCIT_C118467 http://purl.obolibrary.org/obo/NCIT_C132009 http://purl.obolibrary.org/obo/NCIT_C126659 |
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Is_Value_For_GDC_Property | ||
label |
Hand-Schuller-Christian Disease |
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Legacy Concept Name |
Hand-Schuller-Christian_Disease |
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Maps_To |
Multifocal and unisystemic Langerhans-cell histiocytosis Hand-Schuller-Christian disease 9751/3 |
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Neoplastic_Status |
Undetermined |
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Preferred_Name |
Hand-Schuller-Christian Disease |
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prefixIRI |
NCIT:C6920 |
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prefLabel |
Hand-Schuller-Christian Disease |
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Semantic_Type |
Neoplastic Process |
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UMLS_CUI |
C0268205 |
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subClassOf |