loading...| Preferred Name |
Peripheral T-Cell Lymphoma, Not Otherwise Specified |
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| Synonyms |
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| Definitions |
A heterogenous category of nodal and extranodal mature T-cell lymphomas that do not correspond to any of the specifically defined entities of mature T-cell lymphoma in the 2017 WHO classification. Excluded from this category are tumors with a T follicular helper (TFH) cell phenotype. Variants include lymphoepithelioid lymphoma (Lennert lymphoma) and primary EBV-positive nodal T-cell or NK-cell lymphoma. The follicular variant included in the peripheral T-cell lymphomas, not otherwise specified, in the 2008 edition of the WHO classification has been moved to the category of angioimmunoblastic T-cell lymphoma and other nodal lymphomas of T follicular helper cell origin in the 2017 WHO update. The same is true for a proportion of cases previously designated as the T-zone variant, because they usually have a TFH-cell phenotype. (WHO 2017) |
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| ID |
http://purl.obolibrary.org/obo/NCIT_C4340 |
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| code |
C4340 |
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| Contributing_Source |
CPTAC CTEP CTRP GDC |
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| definition |
A heterogenous category of nodal and extranodal mature T-cell lymphomas that do not correspond to any of the specifically defined entities of mature T-cell lymphoma in the 2017 WHO classification. Excluded from this category are tumors with a T follicular helper (TFH) cell phenotype. Variants include lymphoepithelioid lymphoma (Lennert lymphoma) and primary EBV-positive nodal T-cell or NK-cell lymphoma. The follicular variant included in the peripheral T-cell lymphomas, not otherwise specified, in the 2008 edition of the WHO classification has been moved to the category of angioimmunoblastic T-cell lymphoma and other nodal lymphomas of T follicular helper cell origin in the 2017 WHO update. The same is true for a proportion of cases previously designated as the T-zone variant, because they usually have a TFH-cell phenotype. (WHO 2017) |
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| Display_Name |
Peripheral T-Cell Lymphoma, Not Otherwise Specified |
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| in_subset |
http://purl.obolibrary.org/obo/NCIT_C168658 http://purl.obolibrary.org/obo/NCIT_C168656 http://purl.obolibrary.org/obo/NCIT_C168657 http://purl.obolibrary.org/obo/NCIT_C168655 http://purl.obolibrary.org/obo/NCIT_C158520 http://purl.obolibrary.org/obo/NCIT_C102905 http://purl.obolibrary.org/obo/NCIT_C168662 http://purl.obolibrary.org/obo/NCIT_C168661 http://purl.obolibrary.org/obo/NCIT_C177537 http://purl.obolibrary.org/obo/NCIT_C103133 http://purl.obolibrary.org/obo/NCIT_C156952 http://purl.obolibrary.org/obo/NCIT_C116977 http://purl.obolibrary.org/obo/NCIT_C126659 http://purl.obolibrary.org/obo/NCIT_C118168 |
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| Is_Value_For_GDC_Property | ||
| label |
Peripheral T-Cell Lymphoma, Not Otherwise Specified |
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| Legacy Concept Name |
Unspecified_Peripheral_T-Cell_Lymphoma |
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| Maps_To |
Mature T-cell lymphoma, NOS Peripheral T-cell lymphoma, not classified, extranodal and solid organ sites Peripheral T-cell lymphoma, NOS Peripheral T-cell lymphoma Peripheral T-cell lymphoma, not classified, unspecified site Peripheral T-cell lymphoma, not classified Peripheral T-cell lymphoma, unspecified site, extranodal and solid organ sites 9702/3 |
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| Neoplastic_Status |
Malignant |
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| Preferred_Name |
Peripheral T-Cell Lymphoma, Not Otherwise Specified |
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| prefixIRI |
NCIT:C4340 |
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| prefLabel |
Peripheral T-Cell Lymphoma, Not Otherwise Specified |
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| Semantic_Type |
Neoplastic Process |
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| UMLS_CUI |
C2853959 |
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| subClassOf |