Preferred Name |
Myelodysplastic syndrome |
|
Synonyms |
|
|
Definitions |
A group of myeloid hemopathies characterized by blood cytopenias, marrow dysplasia and a high risk of progression to acute myeloid leukemia (AML). |
|
ID |
http://www.orpha.net/ORDO/Orphanet_52688 |
|
definition |
A group of myeloid hemopathies characterized by blood cytopenias, marrow dysplasia and a high risk of progression to acute myeloid leukemia (AML). |
|
definition_citation |
Orphanet |
|
expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=52688 |
|
has_age_of_onset |
All ages |
|
hasDbXref |
MeSH:D009190 OMIM:614286 MedDRA:10028532 UMLS:C3463824 |
|
label |
Myelodysplastic syndrome |
|
notation |
ORPHA:52688 Clinical group |
|
prefixIRI |
ORDO:Orphanet_52688 |
|
prefLabel |
Myelodysplastic syndrome |
|
present_in |
France AND has_annual_incidence_average_value : 6.4 AND has_annual_incidence_range : 1-9 / 100 000 United States AND has_point_prevalence_average_value : 15.0 AND has_point_prevalence_range : 1-5 / 10 000 Japan AND has_point_prevalence_average_value : 1.35 AND has_point_prevalence_range : 1-9 / 100 000 Spain AND has_annual_incidence_average_value : 8.1 AND has_annual_incidence_range : 1-9 / 100 000 Poland AND has_point_prevalence_average_value : 6.2 AND has_point_prevalence_range : 1-9 / 100 000 Germany AND has_point_prevalence_average_value : 7.0 AND has_point_prevalence_range : 1-9 / 100 000 Europe AND has_point_prevalence_range : 1-9 / 100 000 Poland AND has_annual_incidence_average_value : 1.95 AND has_annual_incidence_range : 1-9 / 100 000 Europe AND has_annual_incidence_average_value : 1.5 AND has_annual_incidence_range : 1-9 / 100 000 Switzerland AND has_annual_incidence_average_value : 3.8 AND has_annual_incidence_range : 1-9 / 100 000 United States AND has_annual_incidence_average_value : 3.35 AND has_annual_incidence_range : 1-9 / 100 000 Romania AND has_annual_incidence_average_value : 0.5 AND has_annual_incidence_range : 1-9 / 1 000 000 Sweden AND has_annual_incidence_average_value : 3.5 AND has_annual_incidence_range : 1-9 / 100 000 Germany AND has_annual_incidence_average_value : 4.15 AND has_annual_incidence_range : 1-9 / 100 000 United Kingdom AND has_annual_incidence_average_value : 8.5 AND has_annual_incidence_range : 1-9 / 100 000 Europe AND has_lifetime_prevalence_average_value : 5.02 AND has_lifetime_prevalence_range : 1-9 / 100 000 Greece AND has_annual_incidence_average_value : 5.4 AND has_annual_incidence_range : 1-9 / 100 000 |
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subClassOf |