Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Idiopathic pulmonary fibrosis

Synonyms

IPF

Definitions

An interstitial lung disease with a poor prognosis, that is characterized by the progressive formation of scar tissue within the lungs in the absence of any known cause.

ID

http://www.orpha.net/ORDO/Orphanet_2032

alternative_term

IPF

definition

An interstitial lung disease with a poor prognosis, that is characterized by the progressive formation of scar tissue within the lungs in the absence of any known cause.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=2032

has_age_of_onset

Adult

has_inheritance

Multigenic/multifactorial

hasDbXref

OMIM:616373

OMIM:616371

OMIM:619611

ICD-10:J84.1

MedDRA:10021240

UMLS:C1800706

MeSH:D054990

ICD-11:CB03.4

OMIM:178500

label

Idiopathic pulmonary fibrosis

notation

ORPHA:2032

part_of

http://www.orpha.net/ORDO/Orphanet_98300

prefixIRI

ORDO:Orphanet_2032

prefLabel

Idiopathic pulmonary fibrosis

present_in

Canada AND has_annual_incidence_average_value : 15.35 AND has_annual_incidence_range : 1-5 / 10 000

France AND has_annual_incidence_average_value : 2.8 AND has_annual_incidence_range : 1-9 / 100 000

United States AND has_point_prevalence_average_value : 6.7 AND has_point_prevalence_range : 1-9 / 100 000

Italy AND has_annual_incidence_average_value : 2.6 AND has_annual_incidence_range : 1-9 / 100 000

France AND has_point_prevalence_average_value : 8.2 AND has_point_prevalence_range : 1-9 / 100 000

Japan AND has_point_prevalence_average_value : 5.9 AND has_point_prevalence_range : 1-9 / 100 000

Worldwide AND has_point_prevalence_average_value : 16.125 AND has_point_prevalence_range : 1-5 / 10 000

United Kingdom AND has_annual_incidence_average_value : 1.2 AND has_annual_incidence_range : 1-9 / 100 000

Canada AND has_point_prevalence_average_value : 29.8 AND has_point_prevalence_range : 1-5 / 10 000

Finland AND has_annual_incidence_average_value : 1.3 AND has_annual_incidence_range : 1-9 / 100 000

Finland AND has_point_prevalence_average_value : 8.6 AND has_point_prevalence_range : 1-9 / 100 000

United States AND has_annual_incidence_average_value : 2.6 AND has_annual_incidence_range : 1-9 / 100 000

Worldwide AND has_annual_incidence_average_value : 5.55 AND has_annual_incidence_range : 1-9 / 100 000

Italy AND has_point_prevalence_average_value : 21.2 AND has_point_prevalence_range : 1-5 / 10 000

United Kingdom AND has_point_prevalence_average_value : 11.6 AND has_point_prevalence_range : 1-5 / 10 000

Korea, Republic of AND has_point_prevalence_average_value : 37.0 AND has_point_prevalence_range : 1-5 / 10 000

Korea, Republic of AND has_annual_incidence_average_value : 13.0 AND has_annual_incidence_range : 1-5 / 10 000

treeView

http://www.orpha.net/ORDO/Orphanet_98300

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/MESH/D054990 MESH LOOM
http://purl.obolibrary.org/obo/DOID_0050156 DTO LOOM
http://purl.obolibrary.org/obo/DOID_0050156 DOID LOOM
http://purl.obolibrary.org/obo/DOID_0050156 BAO LOOM
http://purl.obolibrary.org/obo/DOID_0050156 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_0050156 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_0050156 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_0050156 FNS-H LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D054990 RH-MESH LOOM
http://www.limics.org/hrdo/rdfns#pat_id_7029 HRDO LOOM
http://scai.fraunhofer.de/CSEO#idiopathic_pulmonary_fibrosis CSEO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C08.381.483.487.500 RH-MESH LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_0050156 NATPRO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0085786 OCHV LOOM
http://radlex.org/RID/RID28836 RADLEX LOOM
http://purl.obolibrary.org/obo/NCIT_C35716 BERO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C08.381.765.500 RH-MESH LOOM
http://purl.bioontology.org/ontology/MEDLINEPLUS/C1800706 MEDLINEPLUS LOOM
http://purl.bioontology.org/ontology/ICD9CM/516.31 ICD9CM LOOM
http://purl.bioontology.org/ontology/MEDDRA/10021240 MEDDRA LOOM
http://purl.bioontology.org/ontology/ICD10CM/J84.112 ICD10CM LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/700250006 SNOMEDCT LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/700250006 PNADO LOOM
http://www.ebi.ac.uk/efo/EFO_0000768 EFO LOOM
http://www.phoc.org.cn/pmo/class/PMO_00039148 PMAPP-PMO LOOM
http://www.gamuts.net/entity#idiopathic_pulmonary_fibrosis GAMUTS LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Idiopathic_Pulmonary_Fibrosis CSEO LOOM
http://purl.jp/bio/4/id/200906092918364704 IOBC LOOM
http://purl.bioontology.org/ontology/CSP/4008-0052 CRISP LOOM
http://purl.obolibrary.org/obo/OMIT_0026099 OMIT LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C35716 NCIT LOOM
http://www.gamuts.net/entity#idiopathic_pulmonary_fibrosis GAMUTS REST