loading...| Preferred Name |
Hydrops fetalis |
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| Synonyms |
HF |
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| Definitions |
Hydrops fetalis is a severe and challenging fetal condition usually defined as the excessive accumulation of fetal fluid within the fetal extravascular compartments and body cavities that manifests as edema, pleural and pericardial effusion and ascites. It is the end-stage of a wide variety of disorders. The cause may be immunologic (immune hydrops fetalis, IHF) or non immunologic (non-immune hydrops fetalis, NIHF), depending on the presence or absence of maternal antibodies against fetal red cell antigens (ABO incompatibility or rhesus (Rh) incompatibility). |
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| ID |
http://www.orpha.net/ORDO/Orphanet_1041 |
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| alternative_term |
HF Fetal anasarca Fetal hydrops Generalized fetal edema |
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| definition |
Hydrops fetalis is a severe and challenging fetal condition usually defined as the excessive accumulation of fetal fluid within the fetal extravascular compartments and body cavities that manifests as edema, pleural and pericardial effusion and ascites. It is the end-stage of a wide variety of disorders. The cause may be immunologic (immune hydrops fetalis, IHF) or non immunologic (non-immune hydrops fetalis, NIHF), depending on the presence or absence of maternal antibodies against fetal red cell antigens (ABO incompatibility or rhesus (Rh) incompatibility). |
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| definition_citation |
Orphanet |
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| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=1041 |
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| has_age_of_onset |
Antenatal |
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| has_inheritance |
Not applicable |
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| hasDbXref |
ICD-11:KA85.0 ICD-11:KA85.Y MeSH:D015160 ICD-11:KA85 MedDRA:10020529 ICD-11:KC41.1 UMLS:C0020305 ICD-10:P56.0 OMIM:236750 ICD-10:P83.2 ICD-10:P56.9 |
|
| label |
Hydrops fetalis |
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| notation |
ORPHA:1041 |
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| part_of | ||
| prefixIRI |
ORDO:Orphanet_1041 |
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| prefLabel |
Hydrops fetalis |
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| present_in |
Turkey AND has_birth_prevalence_average_value : 380.0 AND has_birth_prevalence_range : >1 / 1000 Thailand AND has_birth_prevalence_average_value : 180.0 AND has_birth_prevalence_range : >1 / 1000 Ireland AND has_birth_prevalence_average_value : 134.0 AND has_birth_prevalence_range : >1 / 1000 Worldwide AND has_point_prevalence_range : Unknown |
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| treeView | ||
| subClassOf |