National Cancer Institute Thesaurus

Last uploaded: February 23, 2024
Preferred Name

Lymphoplasmacytic Lymphoma

Synonyms

lymphoplasmacytic lymphoma

Lymphoplasmacytic Lymphoma

Lymphoplasmacytoid Lymphoma

Lymphoplasmacytic lymphoma

Immunocytoma, Lymphoplasmacytic Type

LYMPHOMA, LYMPHOPLASMACYTIC, MALIGNANT

Lymphoplasmacytic lymphoma (Waldenstrom macroglobulinemia)

Lymphoma, Plasmacytic

Definitions

A clonal neoplasm of small B-lymphocytes, lymphoplasmacytoid cells, and plasma cells involving the bone marrow, lymph nodes, and the spleen. The majority of patients have a serum IgM paraprotein.

ID

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3212

ALT_DEFINITION

A malignant neoplasm composed of lymphocytes (B-cells), lymphoplasmacytoid cells, and plasma cells.

code

C3212

Concept_In_Subset

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C157711

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168661

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168656

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168662

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C77526

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C88025

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C61410

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C116977

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168658

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C126659

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C118168

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C103133

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C102905

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168655

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168657

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C177537

Contributing_Source

CDISC

CTEP

CTRP

GDC

DEFINITION

A clonal neoplasm of small B-lymphocytes, lymphoplasmacytoid cells, and plasma cells involving the bone marrow, lymph nodes, and the spleen. The majority of patients have a serum IgM paraprotein.

Display_Name

Lymphoplasmacytic Lymphoma

FULL_SYN

lymphoplasmacytic lymphoma

Lymphoplasmacytic Lymphoma

Lymphoplasmacytoid Lymphoma

Lymphoplasmacytic lymphoma

Immunocytoma, Lymphoplasmacytic Type

LYMPHOMA, LYMPHOPLASMACYTIC, MALIGNANT

Lymphoplasmacytic lymphoma (Waldenstrom macroglobulinemia)

Lymphoma, Plasmacytic

ICD-O-3_Code

9671/3

9761/3

Is_Value_For_GDC_Property

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C177621

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C176985

label

Lymphoplasmacytic Lymphoma

Legacy Concept Name

Lymphoplasmacytic_Lymphoma_Waldenstrom_s_Macroglobulinemia

Maps_To

Plasmacytic lymphoma

Malignant lymphoma, lymphoplasmacytoid

Lymphoplasmacytic lymphoma

Malignant lymphoma, plasmacytoid

Malignant lymphoma, lymphoplasmacytic

9671/3

Neoplastic_Status

Malignant

Preferred_Name

Lymphoplasmacytic Lymphoma

prefixIRI

Thesaurus:C3212

Semantic_Type

Neoplastic Process

UMLS_CUI

C0334633

subClassOf

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C171299

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