Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Idiopathic Pulmonary Fibrosis

Synonyms

Idiopathic Pulmonary Fibroses

Cryptogenic Fibrosing Alveolitis

Definitions

A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

ID

http://purl.bioontology.org/ontology/MESH/D054990

altLabel

Idiopathic Pulmonary Fibroses

Fibrocystic Pulmonary Dysplasias

Usual Interstitial Pneumonitis

Fibrocystic Pulmonary Dysplasia

Pneumonitides, Usual Interstitial

Pneumonitis, Usual Interstitial

Cryptogenic Fibrosing Alveolitides

Usual Interstitial Pneumonias

Usual Interstitial Pneumonitides

Pulmonary Fibrosis, Idiopathic

Usual Interstitial Pneumonia

Pulmonary Fibroses, Idiopathic

Idiopathic Pulmonary Fibrosis, Familial

Dysplasia, Fibrocystic Pulmonary

Interstitial Pneumonia, Usual

Familial Idiopathic Pulmonary Fibrosis

Idiopathic Fibrosing Alveolitis, Chronic Form

Pulmonary Dysplasia, Fibrocystic

Fibrosing Alveolitides, Cryptogenic

Interstitial Pneumonitis, Usual

Fibrosing Alveolitis, Cryptogenic

Cryptogenic Fibrosing Alveolitis

AN

PULMONARY FIBROSIS is also available

AQL

BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI

cui

C4721952

C4721509

C1800706

DC

1

definition

A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

DX

20090101

HN

2009

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Machine permutation

2009

MDA

20080708

MMR

20220428

MN

C08.381.483.652.500

notation

D054990

prefLabel

Idiopathic Pulmonary Fibrosis

TERMUI

T833800

T812635

T703058

T703056

T703057

T812633

T812634

T812632

T833799

T843517

TH

OMIM (2013)

NLM (2009)

GHR (2014)

ORD (2010)

tui

T047

subClassOf

http://purl.bioontology.org/ontology/MESH/D011658

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http://purl.bioontology.org/ontology/SCTSPA/426437004 SCTSPA CUI
http://purl.bioontology.org/ontology/OMIM/MTHU025157 OMIM CUI
http://purl.bioontology.org/ontology/MDRGER/10021240 MDRGER CUI
http://purl.bioontology.org/ontology/SNOMEDCT/426437004 SNOMEDCT CUI
http://purl.bioontology.org/ontology/OMIM/178500 OMIM CUI
http://purl.bioontology.org/ontology/RCD/X102v RCD CUI
http://purl.bioontology.org/ontology/OMIM/178500 OMIM CUI
http://purl.bioontology.org/ontology/MEDDRA/10016640 MEDDRA CUI
http://purl.bioontology.org/ontology/WHO/1017 WHO-ART CUI
http://purl.bioontology.org/ontology/MDRGER/10011495 MDRGER CUI
http://purl.bioontology.org/ontology/RCD/XE0Yb RCD CUI
http://purl.bioontology.org/ontology/MDRFRE/10011495 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10001892 MEDDRA CUI
http://purl.bioontology.org/ontology/WHOFRE/1017 WHOFRE CUI
http://purl.bioontology.org/ontology/SNMI/D2-60650 SNMI CUI
http://purl.bioontology.org/ontology/MEDLINEPLUS/C1800706 MEDLINEPLUS CUI
http://purl.bioontology.org/ontology/ICD9CM/516.31 ICD9CM CUI
http://purl.bioontology.org/ontology/MSHFRE/D054990 MSHFRE CUI
http://purl.bioontology.org/ontology/NDFRT/N0000181246 NDFRT CUI
http://purl.bioontology.org/ontology/SCTSPA/700250006 SCTSPA CUI
http://purl.bioontology.org/ontology/MEDDRA/10021240 MEDDRA CUI
http://purl.bioontology.org/ontology/ICD10CM/J84.112 ICD10CM CUI
http://purl.bioontology.org/ontology/ICPC2P/R99019 ICPC2P CUI
http://purl.bioontology.org/ontology/SNOMEDCT/700250006 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MDRFRE/10001892 MDRFRE CUI
http://purl.bioontology.org/ontology/MDRGER/10016641 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10016640 MDRGER CUI
http://purl.bioontology.org/ontology/CST/FIBRO%20LUNG COSTART CUI
http://purl.bioontology.org/ontology/MDRFRE/10021240 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10011495 MEDDRA CUI
http://purl.bioontology.org/ontology/OMIM/178500 OMIM CUI
http://purl.bioontology.org/ontology/MDRFRE/10016641 MDRFRE CUI
http://purl.bioontology.org/ontology/SNMI/D2-60654 SNMI CUI
http://purl.bioontology.org/ontology/MDRFRE/10016640 MDRFRE CUI
http://purl.bioontology.org/ontology/CSP/4008-0052 CRISP CUI
http://purl.bioontology.org/ontology/MDRGER/10001892 MDRGER CUI
http://purl.bioontology.org/ontology/MEDDRA/10016641 MEDDRA CUI
http://purl.obolibrary.org/obo/DOID_0050156 DTO LOOM
http://purl.obolibrary.org/obo/DOID_0050156 DOID LOOM
http://purl.obolibrary.org/obo/DOID_0050156 BAO LOOM
http://purl.obolibrary.org/obo/DOID_0050156 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_0050156 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_0050156 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_0050156 FNS-H LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D054990 RH-MESH LOOM
http://www.limics.org/hrdo/rdfns#pat_id_7029 HRDO LOOM
http://scai.fraunhofer.de/CSEO#idiopathic_pulmonary_fibrosis CSEO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C08.381.483.487.500 RH-MESH LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_0050156 NATPRO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0085786 OCHV LOOM
http://radlex.org/RID/RID28836 RADLEX LOOM
http://purl.obolibrary.org/obo/NCIT_C35716 BERO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C08.381.765.500 RH-MESH LOOM
http://purl.bioontology.org/ontology/MEDLINEPLUS/C1800706 MEDLINEPLUS LOOM
http://www.orpha.net/ORDO/Orphanet_2032 ORDO LOOM
http://purl.bioontology.org/ontology/ICD9CM/516.31 ICD9CM LOOM
http://purl.bioontology.org/ontology/MEDDRA/10021240 MEDDRA LOOM
http://purl.bioontology.org/ontology/ICD10CM/J84.112 ICD10CM LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/700250006 SNOMEDCT LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/700250006 PNADO LOOM
http://www.ebi.ac.uk/efo/EFO_0000768 EFO LOOM
http://www.phoc.org.cn/pmo/class/PMO_00039148 PMAPP-PMO LOOM
http://www.gamuts.net/entity#idiopathic_pulmonary_fibrosis GAMUTS LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Idiopathic_Pulmonary_Fibrosis CSEO LOOM
http://purl.jp/bio/4/id/200906092918364704 IOBC LOOM
http://purl.bioontology.org/ontology/CSP/4008-0052 CRISP LOOM
http://purl.obolibrary.org/obo/OMIT_0026099 OMIT LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C35716 NCIT LOOM