Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Mastocytosis, Systemic

Synonyms

Systemic Mastocytoses

Systemic Mastocytosis, Indolent

Definitions

A group of disorders caused by the abnormal proliferation of MAST CELLS in a variety of extracutaneous tissues including bone marrow, liver, spleen, lymph nodes, and gastrointestinal tract. Systemic mastocytosis is commonly seen in adults. These diseases are categorized on the basis of clinical features, pathologic findings, and prognosis.

ID

http://purl.bioontology.org/ontology/MESH/D034721

altLabel

Systemic Mastocytoses

Mastocytoses, Systemic

Systemic Mast-Cell Diseases

Mastocytoses, Aggressive Systemic

Systemic Mastocytosis

Indolent Systemic Mastocytosis

Systemic Mastocytosis, Aggressive

Systemic Mastocytoses, Aggressive

Aggressive Systemic Mastocytoses

Indolent Systemic Mastocytoses

Systemic Mast-Cell Disease

Systemic Mastocytoses, Indolent

Systemic Mast Cell Disease

Mastocytoses, Indolent Systemic

Aggressive Systemic Mastocytosis

Mastocytosis, Indolent Systemic

Mastocytosis, Aggressive Systemic

Mast-Cell Diseases, Systemic

Mast-Cell Disease, Systemic

Systemic Mastocytosis, Indolent

AQL

BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI

cui

C1112486

C0272203

C0221013

DC

1

definition

A group of disorders caused by the abnormal proliferation of MAST CELLS in a variety of extracutaneous tissues including bone marrow, liver, spleen, lymph nodes, and gastrointestinal tract. Systemic mastocytosis is commonly seen in adults. These diseases are categorized on the basis of clinical features, pathologic findings, and prognosis.

A form of systemic mastocytosis in which patients have impaired organ functions due to multifocal infiltrates of pathological MAST CELLS in bone marrow, liver, spleen, gastrointestinal tract, or skeletal system. The cytomorphology shows a low to high grade.

A form of systemic mastocytosis in which patients experience no pain. It is characterized by the multifocal mast cell filtrates, mostly in skin and bone marrow (<20% MAST CELLS). It has a low cytomorphological grade.

DX

20030101

HN

2003

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Machine permutation

2003

MDA

20020702

MMR

20210707

MN

C20.762.750.750

C04.557.450.565.465.750

notation

D034721

prefLabel

Mastocytosis, Systemic

TERMUI

T471905

T471906

T471648

T476080

TH

NLM (2003)

ORD (2010)

tui

T191

subClassOf

http://purl.bioontology.org/ontology/MESH/D008415

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/ICD10CM/C96.21 ICD10CM CUI
http://purl.bioontology.org/ontology/SCTSPA/397356009 SCTSPA CUI
http://purl.bioontology.org/ontology/SNOMEDCT/397016004 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MDRGER/10056453 MDRGER CUI
http://purl.bioontology.org/ontology/SCTSPA/397358005 SCTSPA CUI
http://purl.bioontology.org/ontology/MSHFRE/D034721 MSHFRE CUI
http://purl.bioontology.org/ontology/PDQ/CDR0000613596 PDQ CUI
http://purl.bioontology.org/ontology/SNOMEDCT/397008008 SNOMEDCT CUI
http://purl.bioontology.org/ontology/SNOMEDCT/716655008 SNOMEDCT CUI
http://purl.bioontology.org/ontology/SCTSPA/397008008 SCTSPA CUI
http://purl.bioontology.org/ontology/SCTSPA/716655008 SCTSPA CUI
http://purl.bioontology.org/ontology/MEDDRA/10056453 MEDDRA CUI
http://purl.bioontology.org/ontology/SNOMEDCT/397358005 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MDRFRE/10056453 MDRFRE CUI
http://purl.bioontology.org/ontology/MDRFRE/10056452 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10056452 MEDDRA CUI
http://purl.bioontology.org/ontology/SNOMEDCT/397356009 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MSHFRE/D034721 MSHFRE CUI
http://purl.bioontology.org/ontology/MDRGER/10056452 MDRGER CUI
http://purl.bioontology.org/ontology/PDQ/CDR0000613597 PDQ CUI
http://purl.bioontology.org/ontology/SCTSPA/70910003 SCTSPA CUI
http://purl.bioontology.org/ontology/ICD10CM/D47.02 ICD10CM CUI
http://purl.bioontology.org/ontology/SNMI/DC-47050 SNMI CUI
http://purl.bioontology.org/ontology/SNOMEDCT/70910003 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MDRGER/10042949 MDRGER CUI
http://purl.bioontology.org/ontology/OMIM/154800 OMIM CUI
http://purl.bioontology.org/ontology/MSHFRE/D034721 MSHFRE CUI
http://purl.bioontology.org/ontology/SNOMEDCT/1255137009 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MEDDRA/10042949 MEDDRA CUI
http://purl.bioontology.org/ontology/PDQ/CDR0000701773 PDQ CUI
http://purl.bioontology.org/ontology/SCTSPA/397016004 SCTSPA CUI
http://purl.bioontology.org/ontology/ICD10CM/D47.02 ICD10CM CUI
http://purl.bioontology.org/ontology/SNOMEDCT/50150000 SNOMEDCT CUI
http://purl.bioontology.org/ontology/SNMI/M-97413 SNMI CUI
http://purl.bioontology.org/ontology/NDFRT/N0000010972 NDFRT CUI
http://purl.bioontology.org/ontology/MDRFRE/10042949 MDRFRE CUI
http://purl.bioontology.org/ontology/SCTSPA/50150000 SCTSPA CUI
http://purl.obolibrary.org/obo/OMIT_0022548 OMIT LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.450.565.465.750 RH-MESH LOOM
http://www.phoc.org.cn/pmo/class/PMO_00037851 PMAPP-PMO LOOM
http://purl.jp/bio/4/id/200906094544872223 IOBC LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D034721 RH-MESH LOOM