Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Frontotemporal Dementia

Synonyms

Hereditary Dysphasic Disinhibition Dementia

Disinhibition-Dementia-Parkinsonism-Amytrophy Complices

Definitions

The most common clinical form of FRONTOTEMPORAL LOBAR DEGENERATION, this dementia presents with personality and behavioral changes often associated with disinhibition, apathy, and lack of insight.

ID

http://purl.bioontology.org/ontology/MESH/D057180

altLabel

Hereditary Dysphasic Disinhibition Dementia

Frontotemporal Lobar Degeneration With Ubiquitin-Positive Inclusions

Pick's Disease, Familial

DDPAC

Disease, Wilhelmsen-Lynch

Semantic Dementia

Semantic Dementias

Frontotemporal Dementias, Ubiquitin-Positive

Dementias, Frontotemporal Lobe (FLDEM)

FTD-PGRN

Dementias, Frontotemporal Lobe

Complex, Disinhibition-Dementia-Parkinsonism-Amyotrophy

Dementias, Frontotemporal

Disinhibition-Dementia-Parkinsonism-Amytrophy Complex

Frontotemporal Lobe Dementia

Dementias, Ubiquitin-Positive Frontotemporal

GRN-Related Frontotemporal Dementias

Frontotemporal Lobe Dementias (FLDEM)

Complex, Disinhibition-Dementia-Parkinsonism-Amytrophy

Dementias, Semantic

FTLD with TDP 43 Pathology

Wilhelmsen Lynch Disease

Frontotemporal Dementias, GRN-Related

Dementia, Frontotemporal, with Parkinsonism

Disinhibition Dementia Parkinsonism Amyotrophy Complex

Diseases, Wilhelmsen-Lynch

Frontotemporal Dementia with Parkinsonism 17

Frontotemporal Dementia, Ubiquitin-Positive

Frontotemporal Lobe Dementia (FLDEM)

Diseases, Familial Pick's

FTLD with TDP-43 Pathology

Wilhelmsen-Lynch Disease

Familial Picks Disease

Lobe Dementias, Frontotemporal

Frontotemporal Dementia with Parkinsonism

Disinhibition-Dementia-Parkinsonism-Amyotrophy Complices

Disease, Familial Pick's

FTLD-17 GRN

Complices, Disinhibition-Dementia-Parkinsonism-Amyotrophy

HDDD2

FTLD-TDP

Dementia, Semantic

Frontotemporal Dementia with Parkinsonism-17

Ubiquitin-Positive Frontotemporal Dementia

Frontotemporal Dementias

FTD-GRN

Dementias, GRN-Related Frontotemporal

HDDD1

Dementia, Frontotemporal

Disinhibition Dementia Parkinsonism Amytrophy Complex

Familial Pick's Disease

Wilhelmsen-Lynch Diseases

GRN-Related Frontotemporal Dementia

Frontotemporal Lobe Dementias

Familial Pick Disease

Dementia, Ubiquitin-Positive Frontotemporal

Multiple System Tauopathy with Presenile Dementia

Frontotemporal Dementia, Ubiquitin Positive

Disinhibition-Dementia-Parkinsonism-Amyotrophy Complex

Dementia, Hereditary Dysphasic Disinhibition

Dementia, Frontotemporal Lobe

GRN Related Frontotemporal Dementia

Lobe Dementia, Frontotemporal

Complices, Disinhibition-Dementia-Parkinsonism-Amytrophy

Pick's Diseases, Familial

Frontotemporal Lobar Degeneration With Ubiquitin Positive Inclusions

Dementia, GRN-Related Frontotemporal

FTDP-17

Familial Pick's Diseases

Frontotemporal Dementia, GRN-Related

Dementia, Frontotemporal Lobe (FLDEM)

Ubiquitin-Positive Frontotemporal Dementias

Disinhibition-Dementia-Parkinsonism-Amytrophy Complices

AQL

BL CF CI CL CO DG DH DI DT EC EH EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH SU TH UR VI

cui

C0338462

C0338451

DC

1

definition

The most common clinical form of FRONTOTEMPORAL LOBAR DEGENERATION, this dementia presents with personality and behavioral changes often associated with disinhibition, apathy, and lack of insight.

DX

20100101

HN

2010

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Machine permutation

2010

Mapped from

http://purl.bioontology.org/ontology/MESH/C566288

http://purl.bioontology.org/ontology/MESH/C563476

http://purl.bioontology.org/ontology/MESH/C567699

http://purl.bioontology.org/ontology/MESH/C579991

http://purl.bioontology.org/ontology/MESH/C563003

MDA

20090706

MMR

20150623

MN

C10.574.950.300.299

F03.615.400.380.299

C10.228.140.380.266.299

C18.452.845.800.300.299

notation

D057180

prefLabel

Frontotemporal Dementia

TERMUI

T812309

T843512

T749902

T843465

T749906

T843508

T843510

T841455

T812307

T841555

T749899

T749901

T749903

T812308

T812698

T843042

T843043

T367225

T749907

T843511

T841457

T841458

T843466

T749900

T812640

T843509

T843467

TH

OMIM (2013)

NLM (2000)

NLM (2010)

GHR (2014)

NLM (2014)

ORD (2010)

tui

T047

T048

subClassOf

http://purl.bioontology.org/ontology/MESH/D057174

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/SCTSPA/230288001 SCTSPA CUI
http://purl.bioontology.org/ontology/OMIM/MTHU003256 OMIM CUI
http://purl.bioontology.org/ontology/SNOMEDCT/230288001 SNOMEDCT CUI
http://purl.bioontology.org/ontology/RCD/X003W RCD CUI
http://purl.bioontology.org/ontology/MSHFRE/D057180 MSHFRE CUI
http://purl.bioontology.org/ontology/OMIM/138945 OMIM CUI
http://purl.bioontology.org/ontology/ICD9CM/331.1 ICD9CM CUI
http://purl.bioontology.org/ontology/MDRFRE/10068968 MDRFRE CUI
http://purl.bioontology.org/ontology/SNOMEDCT/230270009 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MDRGER/10068968 MDRGER CUI
http://purl.bioontology.org/ontology/OMIM/104311 OMIM CUI
http://purl.bioontology.org/ontology/ICD10CM/G31.0 ICD10CM CUI
http://purl.bioontology.org/ontology/OMIM/600274 OMIM CUI
http://purl.bioontology.org/ontology/SCTSPA/230270009 SCTSPA CUI
http://purl.bioontology.org/ontology/OMIM/157140 OMIM CUI
http://purl.bioontology.org/ontology/NDFRT/N0000181125 NDFRT CUI
http://purl.bioontology.org/ontology/MEDDRA/10068968 MEDDRA CUI
http://purl.bioontology.org/ontology/RCD/X0034 RCD CUI
http://purl.bioontology.org/ontology/MSHFRE/D057180 MSHFRE CUI
http://purl.obolibrary.org/obo/HP_0002145 HP LOOM
http://purl.obolibrary.org/obo/MONDO_0017276 EFO LOOM
http://purl.obolibrary.org/obo/HP_0002145 EFO LOOM
http://purl.obolibrary.org/obo/MONDO_0017276 OBA LOOM
http://purl.obolibrary.org/obo/DOID_9255 DOID LOOM
http://purl.obolibrary.org/obo/HP_0002145 OBA LOOM
http://purl.obolibrary.org/obo/MONDO_0017276 MONDO LOOM
http://purl.obolibrary.org/obo/HP_0002145 HP LOOM
urn:agi-folder:frontotemporal_dementia BPT LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Frontotemporal_Dementia CSEO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0338451 OCHV LOOM
http://scai.fraunhofer.de/AlzheimerOntology#Frontotemporal_Dementia ADO LOOM
http://scai.fraunhofer.de/AlzheimerOntology#Frontotemporal_Dementia NIO LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU003256 OMIM LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#30455 OCHV LOOM
http://www.semanticweb.org/ontologies/2012/0/Ontology1325521724189.owl#Frontotemporal_dementia CTO-NDD LOOM
http://purl.obolibrary.org/obo/ND_0000167 NDDO LOOM
http://purl.obolibrary.org/obo/ND_0000167 NIO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C18.452.845.800.300.299 RH-MESH LOOM
http://purl.obolibrary.org/obo/MONDO_0017276 DOVES LOOM
http://identifiers.org/omim/600274 REXO LOOM
http://identifiers.org/omim/600274 GEXO LOOM
http://identifiers.org/omim/600274 RETO LOOM
http://ontriscal#FrontotemporalDementia ONTRISCAL LOOM
http://purl.bioontology.org/ontology/ICD9CM/331.1 ICD9CM LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C84719 NCIT LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/230270009 SNOMEDCT LOOM
http://doe-generated-ontology.com/OntoAD#C0338451 ONTOAD LOOM
http://radlex.org/RID/RID5140 RADLEX LOOM
http://localhost/plosthes.2017-1#11833 PLOSTHES LOOM
http://www.phoc.org.cn/pmo/class/PMO_00038219 PMAPP-PMO LOOM
http://purl.obolibrary.org/obo/NCIT_C84719 BERO LOOM
http://www.orpha.net/ORDO/Orphanet_282 ORDO LOOM
http://purl.obolibrary.org/obo/Frontotemporal_Dementia NND_ND LOOM
http://purl.obolibrary.org/obo/OMIM_600274 CCO LOOM
http://purl.bioontology.org/ontology/ICD10CM/G31.0 ICD10CM LOOM
http://www.semanticweb.org/danielhier/ontologies/2019/3/untitled-ontology-57#frontotemporal_dementia NEO LOOM
http://purl.bioontology.org/ontology/OMIM/600274 OMIM LOOM
http://www.case.edu/PMDO#FrontotemporalDementia PMDO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D057180 RH-MESH LOOM
http://scai.fraunhofer.de/AlzheimerOntology#frontotemporal_dementia ADO LOOM
http://scai.fraunhofer.de/AlzheimerOntology#frontotemporal_dementia NIO LOOM
http://www.semanticweb.org/rbmor/ontologies/2021/1/1/untitled-ontology-133#Frontotemporal_Dementia PARTUMDO LOOM
http://www.semanticweb.org/zhenyuzhang/ontologies/2020/DRPSNPTO/FrontotemporalDementia DRPSNPTO LOOM
http://www.limics.fr/ontologies/ontoparonmed#DemenceFrontoTemporale_Signe ONTOPARON LOOM
http://purl.obolibrary.org/obo/DOID_10216 CLO LOOM
http://purl.obolibrary.org/obo/DOID_9255 INBANCIDO LOOM
http://purl.obolibrary.org/obo/DOID_9255 DTO LOOM
http://purl.obolibrary.org/obo/DOID_9255 BAO LOOM
http://purl.obolibrary.org/obo/DOID_9255 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_9255 CIDO LOOM
http://purl.obolibrary.org/obo/DOID_9255 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_9255 FNS-H LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C10.574.950.300.299 RH-MESH LOOM
http://purl.bioontology.org/ontology/MEDDRA/10068968 MEDDRA LOOM
http://purl.bioontology.org/ontology/RCD/X0034 RCD LOOM
http://purl.obolibrary.org/obo/HP_0002145 UPHENO LOOM
http://www.semanticweb.org/zhenyuzhang/ontologies/2021/DREAMDNPTO#FrontotemporalDementia DREAMDNPTO LOOM
http://www.limics.org/hrdo/rdfns#pat_id_3338 HRDO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C10.228.140.380.266.299 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#F03.087.400.380.299 RH-MESH LOOM
http://purl.jp/bio/4/id/200906064813524435 IOBC LOOM
http://purl.obolibrary.org/obo/OMIT_0026899 OMIT LOOM