Preferred Name |
Cryptogenic Organizing Pneumonia |
|
Synonyms |
idiopathic bronchiolitis obliterans with organizing pneumonia cryptogenic organizing pneumonia organizing pneumonia Organizing Pneumonia cryptogenic organizing pneumonitis bronchiolitis obliterans organising pneumonia organising pneumonia cryptogenic organising pneumonitis bronchiolitis obliterans organizing pneumonia idiopathic bronchiolitis obliterans with organising pneumonia COP constrictive bronchiolitis idiopathic BOOP idiopathic bronchiolitis obliterans organising pneumonia idiopathic bronchiolitis obliterans organizing pneumonia |
|
Definitions |
An interstitial lung disease of unknown etiology, occurring between 21-80 years of age. It is characterized by a dramatic onset of a "pneumonia-like" illness with cough, fever, malaise, fatigue, and weight loss. Pathological features include prominent interstitial inflammation without collagen fibrosis, diffuse fibroblastic foci, and no microscopic honeycomb change. There is excessive proliferation of granulation tissue within small airways and alveolar ducts. Cryptogenic organizing pneumonia (COP) is a form of idiopathic interstitial pneumonia characterized pathologically by organizing pneumonia (OP) that presents with non-specific flu-like symptoms, as well as cough and dyspnea and where no etiological agent is found. |
|
ID |
http://www.ebi.ac.uk/efo/EFO_1001300 |
|
database_cross_reference |
MeSH:D018549 MedDRA:10011496 NCIt:C62586 ICD10:J84.116 ICD9:516.36 DOID:2798 NORD:873 UMLS:C0242770 MESH:D018549 GARD:1620 MONDO:0015264 SCTID:68409003 Orphanet:1302 SCTID:719218000 ICD10CM:J84.116 DOID:0050157 NCIT:C62586 |
|
definition |
An interstitial lung disease of unknown etiology, occurring between 21-80 years of age. It is characterized by a dramatic onset of a "pneumonia-like" illness with cough, fever, malaise, fatigue, and weight loss. Pathological features include prominent interstitial inflammation without collagen fibrosis, diffuse fibroblastic foci, and no microscopic honeycomb change. There is excessive proliferation of granulation tissue within small airways and alveolar ducts. Cryptogenic organizing pneumonia (COP) is a form of idiopathic interstitial pneumonia characterized pathologically by organizing pneumonia (OP) that presents with non-specific flu-like symptoms, as well as cough and dyspnea and where no etiological agent is found. |
|
exactMatch |
http://purl.obolibrary.org/obo/DOID_0050157 http://purl.obolibrary.org/obo/Orphanet_1302 http://purl.bioontology.org/ontology/ICD10CM/J84.116 http://linkedlifedata.com/resource/umls/id/C0242770 http://identifiers.org/snomedct/719218000 http://purl.obolibrary.org/obo/NCIT_C62586 |
|
has_exact_synonym |
idiopathic bronchiolitis obliterans with organizing pneumonia cryptogenic organizing pneumonia organizing pneumonia Organizing Pneumonia cryptogenic organizing pneumonitis bronchiolitis obliterans organising pneumonia organising pneumonia cryptogenic organising pneumonitis bronchiolitis obliterans organizing pneumonia idiopathic bronchiolitis obliterans with organising pneumonia COP |
|
has_related_synonym |
constrictive bronchiolitis idiopathic BOOP idiopathic bronchiolitis obliterans organising pneumonia idiopathic bronchiolitis obliterans organizing pneumonia |
|
IAO_0000233 | ||
id |
EFO:1001300 |
|
in_subset |
http://purl.obolibrary.org/obo/mondo#ordo_disease http://purl.obolibrary.org/obo/mondo#rare http://purl.obolibrary.org/obo/mondo#nord_rare |
|
label |
Cryptogenic Organizing Pneumonia |
|
notation |
EFO:1001300 |
|
prefLabel |
Cryptogenic Organizing Pneumonia |
|
term editor |
Sirarat Sarntivijai |
|
subClassOf |