Experimental Factor Ontology

Last uploaded: April 15, 2024
Preferred Name

Cryptogenic Organizing Pneumonia

Synonyms

idiopathic bronchiolitis obliterans with organizing pneumonia

cryptogenic organizing pneumonia

organizing pneumonia

Organizing Pneumonia

cryptogenic organizing pneumonitis

bronchiolitis obliterans organising pneumonia

organising pneumonia

cryptogenic organising pneumonitis

bronchiolitis obliterans organizing pneumonia

idiopathic bronchiolitis obliterans with organising pneumonia

COP

constrictive bronchiolitis

idiopathic BOOP

idiopathic bronchiolitis obliterans organising pneumonia

idiopathic bronchiolitis obliterans organizing pneumonia

Definitions

An interstitial lung disease of unknown etiology, occurring between 21-80 years of age. It is characterized by a dramatic onset of a "pneumonia-like" illness with cough, fever, malaise, fatigue, and weight loss. Pathological features include prominent interstitial inflammation without collagen fibrosis, diffuse fibroblastic foci, and no microscopic honeycomb change. There is excessive proliferation of granulation tissue within small airways and alveolar ducts. Cryptogenic organizing pneumonia (COP) is a form of idiopathic interstitial pneumonia characterized pathologically by organizing pneumonia (OP) that presents with non-specific flu-like symptoms, as well as cough and dyspnea and where no etiological agent is found.

ID

http://www.ebi.ac.uk/efo/EFO_1001300

database_cross_reference

MeSH:D018549

MedDRA:10011496

NCIt:C62586

ICD10:J84.116

ICD9:516.36

DOID:2798

NORD:873

UMLS:C0242770

MESH:D018549

GARD:1620

MONDO:0015264

SCTID:68409003

Orphanet:1302

SCTID:719218000

ICD10CM:J84.116

DOID:0050157

NCIT:C62586

definition

An interstitial lung disease of unknown etiology, occurring between 21-80 years of age. It is characterized by a dramatic onset of a "pneumonia-like" illness with cough, fever, malaise, fatigue, and weight loss. Pathological features include prominent interstitial inflammation without collagen fibrosis, diffuse fibroblastic foci, and no microscopic honeycomb change. There is excessive proliferation of granulation tissue within small airways and alveolar ducts.

Cryptogenic organizing pneumonia (COP) is a form of idiopathic interstitial pneumonia characterized pathologically by organizing pneumonia (OP) that presents with non-specific flu-like symptoms, as well as cough and dyspnea and where no etiological agent is found.

exactMatch

http://purl.obolibrary.org/obo/DOID_0050157

http://purl.obolibrary.org/obo/Orphanet_1302

http://purl.bioontology.org/ontology/ICD10CM/J84.116

http://linkedlifedata.com/resource/umls/id/C0242770

http://identifiers.org/snomedct/719218000

http://purl.obolibrary.org/obo/NCIT_C62586

http://identifiers.org/snomedct/68409003

http://identifiers.org/mesh/D018549

has_exact_synonym

idiopathic bronchiolitis obliterans with organizing pneumonia

cryptogenic organizing pneumonia

organizing pneumonia

Organizing Pneumonia

cryptogenic organizing pneumonitis

bronchiolitis obliterans organising pneumonia

organising pneumonia

cryptogenic organising pneumonitis

bronchiolitis obliterans organizing pneumonia

idiopathic bronchiolitis obliterans with organising pneumonia

COP

has_related_synonym

constrictive bronchiolitis

idiopathic BOOP

idiopathic bronchiolitis obliterans organising pneumonia

idiopathic bronchiolitis obliterans organizing pneumonia

IAO_0000233

https://github.com/monarch-initiative/mondo/issues/4417

id

EFO:1001300

in_subset

http://purl.obolibrary.org/obo/mondo#ordo_disease

http://purl.obolibrary.org/obo/mondo#rare

http://purl.obolibrary.org/obo/mondo#nord_rare

http://purl.obolibrary.org/obo/mondo#orphanet_rare

http://purl.obolibrary.org/obo/mondo#gard_rare

label

Cryptogenic Organizing Pneumonia

notation

EFO:1001300

prefLabel

Cryptogenic Organizing Pneumonia

term editor

Sirarat Sarntivijai

subClassOf

http://purl.obolibrary.org/obo/MONDO_0002429

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Delete Mapping To Ontology Source
http://www.ebi.ac.uk/efo/EFO_1001300 CCONT SAME_URI
http://www.ebi.ac.uk/efo/EFO_1001300 HSPO SAME_URI
http://purl.obolibrary.org/obo/DOID_0050157 DOID LOOM
http://purl.obolibrary.org/obo/MONDO_0015264 MONDO LOOM
http://www.ebi.ac.uk/efo/EFO_1001300 CCONT LOOM
http://www.ebi.ac.uk/efo/EFO_1001300 HSPO LOOM
http://purl.obolibrary.org/obo/DOID_0050157 PNADO LOOM
http://purl.obolibrary.org/obo/DOID_0050157 BAO LOOM
http://purl.obolibrary.org/obo/DOID_0050157 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_0050157 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_0050157 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_0050157 FNS-H LOOM
http://purl.bioontology.org/ontology/ICD9CM/516.36 ICD9CM LOOM
http://purl.bioontology.org/ontology/ICD9CM/516.36 NLMVS LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C08.127.446.135.140.200 RH-MESH LOOM
http://purl.bioontology.org/ontology/MESH/D018549 MESH LOOM
http://purl.bioontology.org/ontology/ICD10CM/J84.116 NLMVS LOOM
http://purl.bioontology.org/ontology/ICD10CM/J84.116 ICD10CM LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D018549 RH-MESH LOOM
http://purl.bioontology.org/ontology/MEDDRA/10011496 MEDDRA LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_0050157 NATPRO LOOM
http://www.limics.org/hrdo/rdfns#pat_id_7034 HRDO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/719218000 SNOMEDCT LOOM
http://purl.obolibrary.org/obo/OMIT_0018739 OMIT LOOM
http://www.gamuts.net/entity#cryptogenic_organizing_pneumonia GAMUTS LOOM
http://radlex.org/RID/RID5335 RADLEX LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C08.381.483.487.249 RH-MESH LOOM
http://purl.obolibrary.org/obo/MONDO_0015264 DOVES LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Cryptogenic_Organizing_Pneumonia CSEO LOOM
http://purl.obolibrary.org/obo/NCIT_C62586 BERO LOOM
http://id.nlm.nih.gov/mesh/D018549 MDM LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C08.381.495.146.135.140.200 RH-MESH LOOM
http://www.orpha.net/ORDO/Orphanet_1302 ORDO LOOM
http://www.phoc.org.cn/pmo/class/PMO_00039147 PMAPP-PMO LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C62586 NCIT LOOM