Preferred Name

Paroxysmal cold hemoglobinuria

Synonyms

Cold agglutinin hemoglobinuria

Cold Donath Landsteiner type autoimmune haemolytic anaemia

Cold Donath Landsteiner type autoimmune hemolytic anemia

Cold hemoglobinuria

PCH - Paroxysmal cold haemoglobinuria

PCH - Paroxysmal cold hemoglobinuria

Paroxysmal cold haemoglobinuria

Cold agglutinin haemoglobinuria

Paroxysmal cold hemoglobinuria (disorder)

ID

127057004

Full Id

http://purl.bioontology.org/ontology/SNOMEDCT/127057004

CONCEPTSTATUS

0

CTV3ID

XU6se

has_causative_agent

Antibody

has_clinical_course

Sudden onset AND/OR short duration

has_definitional_manifestation

Immune system finding

Hemolysis

Erythropenia

has_episodicity

Episodicities

has_pathological_process

Autoimmune

has_severity

Severities

inverse_may_be_a

Cold autoimmune hemolytic anemia

Hemoglobinuria: [due to hemolysis from external cause NOS] or [cold] or [acquired hemolytic anemia with hemoglobinuria NEC] or [paroxysmal NOS]

Cold Donath Landsteiner type autoimmune hemolytic anemia

Cold hemagglutinin disease

isa

Acute disease

Autoimmune hemolytic anemia

ISPRIMITIVE

1

Semantic_Type

Disease or Syndrome

SNOMEDID

DC-36451

SYNONYM FN

Paroxysmal cold hemoglobinuria (disorder)

SYNONYM PTGB

Paroxysmal cold haemoglobinuria

SYNONYM SY

Cold agglutinin hemoglobinuria

Cold Donath Landsteiner type autoimmune hemolytic anemia

Cold hemoglobinuria

PCH - Paroxysmal cold hemoglobinuria

SYNONYM SYGB

Cold Donath Landsteiner type autoimmune haemolytic anaemia

PCH - Paroxysmal cold haemoglobinuria

Cold agglutinin haemoglobinuria

TUI

T047

UMLS_CUI

C0086774

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